电话:
400-7060-959
传真:
+86 10 56315212-8813
电子邮件:
orders@antibodies-online.cn

CSTB Protein (AA 1-98, full length) (GST tag)

CSTB 宿主: 人 宿主: 大肠杆菌(E. Coli) Recombinant 95 % SDS, WB, ELISA
产品编号 ABIN7479584
发货至: 中国
  • 抗原 See all CSTB 蛋白
    CSTB (Cystatin B (Stefin B) (CSTB))
    蛋白类型
    Recombinant
    产品特性
    AA 1-98, full length
    宿主
    • 5
    • 3
    • 3
    • 3
    • 1
    • 1
    • 1
    • 1
    • 1
    资源
    • 9
    • 7
    • 1
    • 1
    • 1
    大肠杆菌(E. Coli)
    标记
    This CSTB protein is labelled with GST tag.
    应用范围
    SDS-PAGE (SDS), Western Blotting (WB), ELISA
    序列
    MMCGAPSATQ PATAETQHIA DQVRSQLEEK ENKKFPVFKA VSFKSQVVAG TNYFIKVHVG DEDFVHLRVF QSLPHENKPL TLSNYQTNKA KHDELTYF
    纯度
    95 %
    Top Product
    Discover our top product CSTB 蛋白
  • 限制
    仅限研究用
  • 状态
    Lyophilized
    缓冲液
    PBS buffer, 20mM GSH.
    储存条件
    4 °C
  • 抗原
    CSTB (Cystatin B (Stefin B) (CSTB))
    别名
    Cystatin-B (CSTB 产品)
    别名
    CST6 Protein, EPM1 Protein, EPM1A Protein, PME Protein, STFB Protein, ULD Protein, CSTB Protein, Cyb Protein, Epm1 Protein, Stfb Protein, MGC189005 Protein, pme Protein, cst6 Protein, epm1 Protein, stfb Protein, AA960480 Protein, ARABIDOPSIS THALIANA PHYTOCYSTATIN 6 Protein, ATCYS6 Protein, ATCYSB Protein, cystatin B Protein, LOC100008600 Protein, LOC100136235 Protein, CPI1 Protein, cystatin B Protein, cystatin B (stefin B) Protein, cystatin 14a, tandem duplicate 2 Protein, cystatin-B Protein, CSTB Protein, Cstb Protein, cstb Protein, cst14a.2 Protein, CYSB Protein, cpi1 Protein, LOC101123265 Protein
    背景
    Background: This is an intracellular thiol proteinase inhibitor. Tightly binding reversible inhibitor of cathepsins L, H and B. Defects in CSTB are the cause of progressive myoclonic epilepsy type 1 (EPM1) [MIM:254800]. EPM1 is an autosomal recessive disorder characterized by severe, stimulus-sensitive myoclonus and tonic-clonic seizures. The onset, occurring between 6 and 13 years of age, is characterized by convulsions. Myoclonus begins 1 to 5 years later. The twitchings occur predominantly in the proximal muscles of the extremities and are bilaterally symmetrical, although asynchronous. At first small, they become late in the clinical course so violent that the victim is thrown to the floor. Mental deterioration and eventually dementia develop. Synonyms: CPI-B Liver thiol proteinase inhibitor Stefin-B.
    分子量
    38.5 kD
    NCBI登录号
    NM_000100
    UniProt
    P04080
    途径
    Response to Water Deprivation
You are here:
客服