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Ataxin 3 抗体

(Ataxin 3 (ATXN3))
Machado-Joseph disease, also known as spinocerebellar ataxia-3, is an autosomal dominant neurologic disorder. The protein encoded by this gene contains (CAG)n repeats in the coding region, and the expansion of these repeats from the normal 13-36 to 68-79 is one cause of Machado-Joseph disease. There is a negative correlation between the age of onset and CAG repeat numbers. Alternatively spliced transcript variants encoding different isoforms have been described for this gene. [provided by RefSeq, Sep 2009].

58 results :

ATXN3 适用: 人 WB, IHC, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN3021829
 
ATXN3 适用: 人 WB, IHC (p), IP 宿主: 兔 Polyclonal unconjugated
Pubmed 1 reference
产品编号 ABIN2856981
 
ATXN3 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7144793
 
KO Validated ATXN3 适用: 人 WB, IF, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2854322
 
ATXN3 适用: 人 WB, IHC (p), FACS 宿主: 兔 Polyclonal RB23951 unconjugated
产品编号 ABIN653191
 
ATXN3 适用: 人 WB, IHC (p), FACS, EIA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN950546
 
ATXN3 适用: 人, 小鼠, 大鼠, Cow, 绵羊, 马, 兔, 豚鼠, 犬, 斑马鱼 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2784210
 
ATXN3 适用: 人, 小鼠, 大鼠, Cow, 绵羊, 马, 兔, 豚鼠, 犬, 猴, Pig, Cat, 小鸡, 驴, 山羊, Hamster, Avian WB 宿主: 山羊 Polyclonal unconjugated
产品编号 ABIN6254159
 
ATXN3 适用: 人, 小鼠, 大鼠, Cow, 绵羊, 马, 猴, Pig WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6755320
 
ATXN3 适用: 人, 大鼠 WB, IHC, IF, FACS, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN3043796
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, IF, IC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7307550
 
ATXN3 适用: 人 WB, IHC (p), EIA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN357621
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC (p), IF (cc), IF (p), ICC, IHC (fro) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6989198
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC (p), IHC (fro) 宿主: 兔 Polyclonal Biotin
产品编号 ABIN6982636
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 647
产品编号 ABIN6980031
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 350
产品编号 ABIN6976655
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 680
产品编号 ABIN6980938
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 594
产品编号 ABIN6979185
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 750
产品编号 ABIN6981910
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 488
产品编号 ABIN6977516
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • ELISA
    • Immunohistochemistry (IHC)
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Flow Cytometry (FACS)
    • Immunofluorescence (IF)
    • Immunocytochemistry (ICC)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Immunoprecipitation (IP)
    • Enzyme Immunoassay (EIA)
    • Immunochromatography (IC)
    • Immunohistochemistry (Formalin-fixed Paraffin-embedded Sections) (IHC (fp))
  • 适用
    • Human
    • Mouse
    • Rat
    • Cow
    • Horse
    • Sheep
    • Dog
    • Guinea Pig
    • Monkey
    • Pig
    • Rabbit
    • Cat
    • Chicken
    • Donkey
    • Goat
    • Hamster
    • Avian
    • Zebrafish (Danio rerio)
  • 论文引用
  • 图像
  • Preservative free only
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Goat
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 2SCA-1H9
    • RB23951
    • RB4606
  • 抗原表位
    • AA 51-150
    • AA 29-59
    • AA 1-288
    • pSer256
    • AA 267-297
    • N-Term
    • AA 1-245
    • AA 120-250
    • C-Term
    • AA 1-182
    • AA 1-215
    • AA 1-364
    • AA 200-280
    • AA 226-254
    • AA 261-288
    • AA 35-84
    • Middle Region
  • 标记
    • 非结合性
    • FITC
    • HRP
    • Biotin
    • PE
    • APC
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
  • 抗体亚型
    • IgG
    • Ig Fraction
    • IgG1 kappa
  • Format
    • Liquid
    • Lyophilized
  • Grade
    • KO Validated
  • Supplier
    • antibodies-online
    • Signalway
    • Abbexa
    • Abcepta
    • Acris
    • Aviva Systems Biology
    • Biomatik
    • Boster Bio
    • Cohesion Biosciences
    • ProteoGenix
    • RayBiotech
    • USBio

Latest Publications for our Ataxin 3 抗体

Hsu, Jhang, Cheng, Chang, Mao, Yang, Lin, Chen, Yang: "The Truncated C-terminal Fragment of Mutant ATXN3 Disrupts Mitochondria Dynamics in Spinocerebellar Ataxia Type 3 Models." in: Frontiers in molecular neuroscience, Vol. 10, pp. 196, (2017) (PubMed).

Zeng, Tang, Ma: "Ataxin-3 expression correlates with the clinicopathologic features of gastric cancer." in: International journal of clinical and experimental medicine, Vol. 7, Issue 4, pp. 973-81, (2014) (PubMed).

Michlewski, Krzyzosiak: "Molecular architecture of CAG repeats in human disease related transcripts." in: Journal of molecular biology, Vol. 340, Issue 4, pp. 665-79, (2004) (PubMed).

Li, Yokota, Matsumura, Taira, Mizusawa: "Sequence-dependent and independent inhibition specific for mutant ataxin-3 by small interfering RNA." in: Annals of neurology, Vol. 56, Issue 1, pp. 124-9, (2004) (PubMed).

Albrecht, Golatta, Wüllner, Lengauer: "Structural and functional analysis of ataxin-2 and ataxin-3." in: European journal of biochemistry / FEBS, Vol. 271, Issue 15, pp. 3155-70, (2004) (PubMed).

Aspberg, Miura, Bourdoulous, Shimonaka, Heinegârd, Schachner, Ruoslahti, Yamaguchi: "The C-type lectin domains of lecticans, a family of aggregating chondroitin sulfate proteoglycans, bind tenascin-R by protein-protein interactions independent of carbohydrate moiety." in: Proceedings of the National Academy of Sciences of the United States of America, Vol. 94, Issue 19, pp. 10116-21, (1997) (PubMed).

Paulson, Das, Crino, Perez, Patel, Gotsdiner, Fischbeck, Pittman: "Machado-Joseph disease gene product is a cytoplasmic protein widely expressed in brain." in: Annals of neurology, Vol. 41, Issue 4, pp. 453-62, (1997) (PubMed).

Aliases for Ataxin 3 抗体

ataxin 3 (atxn3) 抗体
ataxin 3 (ATXN3) 抗体
ataxin 3 L homeolog (atxn3.L) 抗体
ataxin-3 (MICPUN_104046) 抗体
ataxin-3 (MICPUCDRAFT_46658) 抗体
ataxin 3 (Atxn3) 抗体
2210008M02Rik 抗体
AI463012 抗体
AI647473 抗体
at3 抗体
AT3 抗体
ataxin-3 抗体
atx3 抗体
ATX3 抗体
ATXN3 抗体
jos 抗体
JOS 抗体
MGC83584 抗体
Mjd 抗体
mjd 抗体
MJD 抗体
mjd1 抗体
MJD1 抗体
Rsca3 抗体
sca3 抗体
SCA3 抗体
Sca3 抗体
zgc:56323 抗体
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