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Ataxin 3 抗体

(Ataxin 3 (ATXN3))
Machado-Joseph disease, also known as spinocerebellar ataxia-3, is an autosomal dominant neurologic disorder. The protein encoded by this gene contains (CAG)n repeats in the coding region, and the expansion of these repeats from the normal 13-36 to 68-79 is one cause of Machado-Joseph disease. There is a negative correlation between the age of onset and CAG repeat numbers. Alternatively spliced transcript variants encoding different isoforms have been described for this gene. [provided by RefSeq, Sep 2009].

72 results

ATXN3 适用: 人, 小鼠 WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1833855
100 μL
发货至: 中国
获取报价
 
ATXN3 适用: 人, 大鼠, 小鼠 IHC, IF, FACS 宿主: 兔 Monoclonal A135 unconjugated Recombinant Antibody
产品编号 ABIN7828027
50 μL
发货至: 中国
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ATXN3 适用: 人, 大鼠, 小鼠, Cow, 绵羊, 马, 兔, 豚鼠, 犬, 猴, Pig, Cat, 小鸡, 驴, 山羊, Hamster WB 宿主: 山羊 Polyclonal unconjugated
产品编号 ABIN2617361
600 μg
发货至: 中国
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ATXN3 适用: 人, 大鼠, 小鼠 WB, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6388309
100 μL (More quantities available)
发货至: 中国
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ATXN3 适用: 人, 大鼠, 小鼠 WB, IHC, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7307550
100 μL (More quantities available)
发货至: 中国
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ATXN3 适用: 人 WB, IHC (p), EIA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN357621
400 μL
发货至: 中国
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ATXN3 适用: 人, 大鼠 WB, ELISA, IHC 宿主: 兔 Polyclonal Biotin
产品编号 ABIN7970568
 
ATXN3 适用: 人, 大鼠 FACS 宿主: 兔 Polyclonal Cy3
产品编号 ABIN7970569
 
ATXN3 适用: 人, 大鼠 FACS 宿主: 兔 Polyclonal Fluoro488
产品编号 ABIN7970570
 
ATXN3 适用: 人, 大鼠 FACS 宿主: 兔 Polyclonal Fluoro550
产品编号 ABIN7970571
 
ATXN3 适用: 人, 大鼠 FACS 宿主: 兔 Polyclonal Fluoro594
产品编号 ABIN7970572
 
Carrier-free ATXN3 适用: 人, 大鼠 WB, IHC, IF, FACS, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7970578
 
ATXN3 适用: 人, 大鼠 WB, ELISA, IHC 宿主: 兔 Polyclonal HRP
产品编号 ABIN7970574
 
ATXN3 适用: 人, 大鼠 FACS 宿主: 兔 Polyclonal APC
产品编号 ABIN7970575
 
ATXN3 适用: 人, 大鼠 FACS 宿主: 兔 Polyclonal PE
产品编号 ABIN7970576
 
ATXN3 适用: 人, 大鼠 FACS 宿主: 兔 Polyclonal Fluoro647
产品编号 ABIN7970577
 
ATXN3 适用: 人, 大鼠 FACS 宿主: 兔 Polyclonal FITC
产品编号 ABIN7970573
 
ATXN3 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2205695
200 μL
发货至: 中国
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ATXN3 适用: 人 WB, IHC (fp) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2800585
100 μL
发货至: 中国
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ATXN3 适用: 人 WB, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1885789
100 μL
发货至: 中国
获取报价
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • Immunohistochemistry (IHC)
    • ELISA
    • Flow Cytometry (FACS)
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunofluorescence (IF)
    • Immunocytochemistry (ICC)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Immunoprecipitation (IP)
    • Enzyme Immunoassay (EIA)
    • Immunochromatography (IC)
    • Immunohistochemistry (Formalin-fixed Paraffin-embedded Sections) (IHC (fp))
  • 适用
    • Human
    • Rat
    • Mouse
    • Cow
    • Horse
    • Sheep
    • Dog
    • Guinea Pig
    • Monkey
    • Pig
    • Rabbit
    • Cat
    • Chicken
    • Donkey
    • Goat
    • Hamster
    • Avian
    • Zebrafish (Danio rerio)
  • 论文引用
  • 图像
  • 仅无防腐剂
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Goat
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 2SCA-1H9
    • A135
    • RB23951
    • RB4606
  • 抗原表位
    • AA 51-150
    • C-Term
    • AA 29-59
    • pSer256
    • AA 1-288
    • AA 267-297
    • N-Term
    • AA 1-245
    • AA 120-250
    • AA 200-280
    • AA 261-288
    • AA 1-182
    • AA 1-215
    • AA 1-364
    • AA 35-84
    • Middle Region
  • 标记
    • 非结合性
    • FITC
    • HRP
    • Biotin
    • PE
    • APC
    • Cy3
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • Cy5
    • Cy5.5
    • Cy7
    • Fluoro488
    • Fluoro550
    • Fluoro594
    • Fluoro647
  • 抗体亚型
    • IgG
    • Ig Fraction
    • IgG1 kappa
    • kappa
  • 蛋白类型
    • Recombinant Antibody
  • Format
    • Liquid
    • Lyophilized
  • Grade
    • Carrier-free
    • KO Validated
  • Supplier
    • antibodies-online
    • Boster Bio
    • Signalway
    • Abbexa
    • Acris
    • ProteoGenix
    • Aviva Systems Biology
    • Cohesion Biosciences
    • NSJ Bioreagents
    • RayBiotech
    • USBio

Latest Publications for our Ataxin 3 抗体

Hsu, Jhang, Cheng, Chang, Mao, Yang, Lin, Chen, Yang: "The Truncated C-terminal Fragment of Mutant ATXN3 Disrupts Mitochondria Dynamics in Spinocerebellar Ataxia Type 3 Models." in: Frontiers in molecular neuroscience, Vol. 10, pp. 196, (2017) (PubMed).

Zeng, Tang, Ma: "Ataxin-3 expression correlates with the clinicopathologic features of gastric cancer." in: International journal of clinical and experimental medicine, Vol. 7, Issue 4, pp. 973-81, (2014) (PubMed).

Michlewski, Krzyzosiak: "Molecular architecture of CAG repeats in human disease related transcripts." in: Journal of molecular biology, Vol. 340, Issue 4, pp. 665-79, (2004) (PubMed).

Li, Yokota, Matsumura, Taira, Mizusawa: "Sequence-dependent and independent inhibition specific for mutant ataxin-3 by small interfering RNA." in: Annals of neurology, Vol. 56, Issue 1, pp. 124-9, (2004) (PubMed).

Albrecht, Golatta, Wüllner, Lengauer: "Structural and functional analysis of ataxin-2 and ataxin-3." in: European journal of biochemistry / FEBS, Vol. 271, Issue 15, pp. 3155-70, (2004) (PubMed).

Aspberg, Miura, Bourdoulous, Shimonaka, Heinegârd, Schachner, Ruoslahti, Yamaguchi: "The C-type lectin domains of lecticans, a family of aggregating chondroitin sulfate proteoglycans, bind tenascin-R by protein-protein interactions independent of carbohydrate moiety." in: Proceedings of the National Academy of Sciences of the United States of America, Vol. 94, Issue 19, pp. 10116-21, (1997) (PubMed).

Paulson, Das, Crino, Perez, Patel, Gotsdiner, Fischbeck, Pittman: "Machado-Joseph disease gene product is a cytoplasmic protein widely expressed in brain." in: Annals of neurology, Vol. 41, Issue 4, pp. 453-62, (1997) (PubMed).

Aliases for Ataxin 3 抗体

ataxin 3 (atxn3) 抗体
ataxin 3 (ATXN3) 抗体
ataxin 3 L homeolog (atxn3.L) 抗体
ataxin-3 (MICPUN_104046) 抗体
ataxin-3 (MICPUCDRAFT_46658) 抗体
ataxin 3 (Atxn3) 抗体
2210008M02Rik 抗体
AI463012 抗体
AI647473 抗体
at3 抗体
AT3 抗体
ataxin-3 抗体
atx3 抗体
ATX3 抗体
ATXN3 抗体
jos 抗体
JOS 抗体
MGC83584 抗体
Mjd 抗体
mjd 抗体
MJD 抗体
mjd1 抗体
MJD1 抗体
Rsca3 抗体
sca3 抗体
SCA3 抗体
Sca3 抗体
zgc:56323 抗体
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