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MCCC2 抗体

MCCC2 适用: 人, 小鼠, 大鼠 IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7384046
发货至: 中国
  • 抗原 See all MCCC2 抗体
    MCCC2 (Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
    适用
    • 47
    • 18
    • 6
    • 3
    • 2
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    人, 小鼠, 大鼠
    宿主
    • 42
    • 6
    克隆类型
    • 46
    • 2
    多克隆
    标记
    • 28
    • 7
    • 4
    • 3
    • 3
    • 3
    This MCCC2 antibody is un-conjugated
    应用范围
    • 48
    • 23
    • 9
    • 6
    • 5
    • 4
    • 3
    • 1
    Immunofluorescence (IF)
    纯化方法
    Affinity purification
    免疫原
    Recombinant fusion protein of human MCCC2 (NP_071415.1).
    亚型
    IgG
    Top Product
    Discover our top product MCCC2 Primary Antibody
  • 应用备注
    IF 1:50-1:100
    限制
    仅限研究用
  • 浓度
    1 mg/mL
    缓冲液
    PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3
    储存液
    Sodium azide
    注意事项
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    储存条件
    -20 °C
    储存方法
    Store at -20°C. Avoid freeze / thaw cycles.
  • 抗原
    MCCC2 (Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
    别名
    MCCC2 (MCCC2 产品)
    别名
    si:dkey-57m14.1 antibody, zgc:85685 antibody, MCCB antibody, 3-METHYLCROTONYL-COA CARBOXYLASE antibody, 3-methylcrotonyl-CoA carboxylase antibody, F28A23.210 antibody, F28A23_210 antibody, 4930552N12Rik antibody, methylcrotonoyl-CoA carboxylase 2 (beta) antibody, methylcrotonoyl-CoA carboxylase 2 antibody, methylcrotonoyl-CoA carboxylase 2 S homeolog antibody, 3-methylcrotonyl-CoA carboxylase antibody, methylcrotonoyl-Coenzyme A carboxylase 2 (beta) antibody, mccc2 antibody, MCCC2 antibody, mccc2.S antibody, Mccc2 antibody, MCCB antibody
    背景
    MCCC2,MCCB,This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.
    基因ID
    64087
    UniProt
    Q9HCC0
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