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MCCC2 抗体 (AA 284-563)

MCCC2 适用: 人 WB, IHC, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7268494
发货至: 中国
  • 抗原 See all MCCC2 抗体
    MCCC2 (Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
    抗原表位
    • 14
    • 8
    • 7
    • 6
    • 3
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    AA 284-563
    适用
    • 47
    • 19
    • 7
    • 3
    • 2
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    宿主
    • 42
    • 6
    克隆类型
    • 46
    • 2
    多克隆
    标记
    • 28
    • 7
    • 4
    • 3
    • 3
    • 3
    This MCCC2 antibody is un-conjugated
    应用范围
    • 47
    • 23
    • 8
    • 6
    • 5
    • 4
    • 3
    • 1
    Western Blotting (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)
    原理
    MCCC2 Rabbit pAb
    序列
    LHLTRKVVRN LNYQKKLDVT IEPSEEPLFP ADELYGIVGA NLKRSFDVRE VIARIVDGSR FTEFKAFYGD TLVTGFARIF GYPVGIVGNN GVLFSESAKK GTHFVQLCCQ RNIPLLFLQN ITGFMVGREY EAEGIAKDGA KMVAAVACAQ VPKITLIIGG SYGAGNYGMC GRAYSPRFLY IWPNARISVM GGEQAANVLA TITKDQRARE GKQFSSADEA ALKEPIIKKF EEEGNPYYSS ARVWDDGIID PADTRLVLGL SFSAALNAPI EKTDFGIFRM
    交叉反应
    人, 小鼠, 大鼠
    产品特性
    Polyclonal Antibodies
    纯化方法
    Affinity purification
    免疫原
    Recombinant fusion protein containing a sequence corresponding to amino acids 284-563 of human MCCC2 (NP_071415.1).
    亚型
    IgG
    Top Product
    Discover our top product MCCC2 Primary Antibody
  • 应用备注
    WB,1:500 - 1:2000,IHC,1:50 - 1:100,IF,1:50 - 1:100
    限制
    仅限研究用
  • 状态
    Liquid
    缓冲液
    PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
    储存液
    Sodium azide
    注意事项
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    储存条件
    -20 °C
    储存方法
    Store at -20°C. Avoid freeze / thaw cycles.
  • 抗原
    MCCC2 (Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
    别名
    MCCC2 (MCCC2 产品)
    别名
    si:dkey-57m14.1 antibody, zgc:85685 antibody, MCCB antibody, 3-METHYLCROTONYL-COA CARBOXYLASE antibody, 3-methylcrotonyl-CoA carboxylase antibody, F28A23.210 antibody, F28A23_210 antibody, 4930552N12Rik antibody, methylcrotonoyl-CoA carboxylase 2 (beta) antibody, methylcrotonoyl-CoA carboxylase 2 antibody, methylcrotonoyl-CoA carboxylase 2 S homeolog antibody, 3-methylcrotonyl-CoA carboxylase antibody, methylcrotonoyl-Coenzyme A carboxylase 2 (beta) antibody, mccc2 antibody, MCCC2 antibody, mccc2.S antibody, Mccc2 antibody, MCCB antibody
    背景
    This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.,MCCC2,MCCB,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,Amino acid metabolism,MCCC2
    分子量
    57kDa/61kDa
    基因ID
    64087
    UniProt
    Q9HCC0
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