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MCCC2 抗体 (AA 1-563)

MCCC2 适用: 人 WB, IF 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN528514
发货至: 中国
  • 抗原 See all MCCC2 抗体
    MCCC2 (Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
    抗原表位
    • 14
    • 8
    • 7
    • 5
    • 3
    • 3
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    AA 1-563
    适用
    • 47
    • 19
    • 7
    • 3
    • 2
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    宿主
    • 43
    • 5
    小鼠
    克隆类型
    • 46
    • 2
    多克隆
    标记
    • 28
    • 7
    • 4
    • 3
    • 3
    • 3
    This MCCC2 antibody is un-conjugated
    应用范围
    • 47
    • 23
    • 9
    • 6
    • 5
    • 4
    • 3
    • 1
    Western Blotting (WB), Immunofluorescence (IF)
    原理
    Mouse polyclonal antibody raised against a full-length human MCCC2 protein.
    序列
    MWAVLRLALR PCARASPAGP RAYHGDSVAS LGTQPDLGSA LYQENYKQMK ALVNQLHERV EHIKLGGGEK ARALHISRGK LLPRERIDNL IDPGSPFLEL SQFAGYQLYD NEEVPGGGII TGIGRVSGVE CMIIANDATV KGGAYYPVTV KKQLRAQEIA MQNRLPCIYL VDSGGAYLPR QADVFPDRDH FGRTFYNQAI MSSKNIAQIA VVMGSCTAGG AYVPAMADEN IIVRKQGTIF LAGPPLVKAA TGEEVSAEDL GGADLHCRKS GVSDHWALDD HHALHLTRKV VRNLNYQKKL DVTIEPSEEP LFPADELYGI VGANLKRSFD VREVIARIVD GSRFTEFKAF YGDTLVTGFA RIFGYPVGIV GNNGVLFSES AKKGTHFVQL CCQRNIPLLF LQNITGFMVG REYEAEGIAK DGAKMVAAVA CAQVPKITLI IGGSYGAGNY GMCGRAYSPR FLYIWPNARI SVMGGEQAAN VLATITKDQR AREGKQFSSA DEAALKEPII KKFEEEGNPY YSSARVWDDG IIDPADTRLV LGLSFSAALN APIEKTDFGI FRM
    交叉反应
    产品特性
    Antibody reactive against mammalian transfected lysate.
    免疫原
    MCCC2 (NP_071415.1, 1 a.a. ~ 563 a.a) full-length human protein.
  • 应用备注
    Optimal working dilution should be determined by the investigator.
    限制
    仅限研究用
  • 缓冲液
    In 1x PBS, pH 7.4
    注意事项
    Aliquot to avoid repeated freezing and thawing.
    储存条件
    -20 °C
    储存方法
    Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
  • Grünert, Stucki, Morscher, Suormala, Bürer, Burda, Christensen, Ficicioglu, Herwig, Kölker, Möslinger, Pasquini, Santer, Schwab, Wilcken, Fowler, Yue, Baumgartner: "3-methylcrotonyl-CoA carboxylase deficiency: clinical, biochemical, enzymatic and molecular studies in 88 individuals." in: Orphanet journal of rare diseases, Vol. 7, pp. 31, (2012) (PubMed).

  • 抗原
    MCCC2 (Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
    别名
    MCCC2 (MCCC2 产品)
    别名
    si:dkey-57m14.1 antibody, zgc:85685 antibody, MCCB antibody, 3-METHYLCROTONYL-COA CARBOXYLASE antibody, 3-methylcrotonyl-CoA carboxylase antibody, F28A23.210 antibody, F28A23_210 antibody, 4930552N12Rik antibody, methylcrotonoyl-CoA carboxylase 2 (beta) antibody, methylcrotonoyl-CoA carboxylase 2 antibody, methylcrotonoyl-CoA carboxylase 2 S homeolog antibody, 3-methylcrotonyl-CoA carboxylase antibody, methylcrotonoyl-Coenzyme A carboxylase 2 (beta) antibody, mccc2 antibody, MCCC2 antibody, mccc2.S antibody, Mccc2 antibody, MCCB antibody
    背景
    Full Gene Name: methylcrotonoyl-Coenzyme A carboxylase 2 (beta)
    Synonyms: MCCB
    基因ID
    64087
    NCBI登录号
    NM_022132
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