电话:
400-7060-959
传真:
+86 10 56315212-8813
电子邮件:
orders@antibodies-online.cn

MCCC2 抗体 (AA 351-450) (HRP)

MCCC2 适用: 人, 小鼠, Xenopus tropicalis WB 宿主: 兔 Polyclonal HRP
产品编号 ABIN6944040
发货至: 中国
  • 抗原 See all MCCC2 抗体
    MCCC2 (Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
    抗原表位
    • 14
    • 8
    • 7
    • 6
    • 3
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    AA 351-450
    适用
    • 47
    • 18
    • 7
    • 2
    • 2
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    人, 小鼠, Xenopus tropicalis
    宿主
    • 42
    • 6
    克隆类型
    • 46
    • 2
    多克隆
    标记
    • 29
    • 7
    • 3
    • 3
    • 3
    • 3
    This MCCC2 antibody is conjugated to HRP
    应用范围
    • 47
    • 23
    • 9
    • 7
    • 5
    • 4
    • 3
    • 1
    Western Blotting (WB)
    交叉反应
    人, 小鼠, Xenopus tropicalis
    预测反应
    Rat,Dog,Cow,Pig,Horse,Rabbit
    纯化方法
    Purified by Protein A.
    免疫原
    KLH conjugated synthetic peptide derived from human MCCC2
    亚型
    IgG
    Top Product
    Discover our top product MCCC2 Primary Antibody
  • 应用备注
    WB 1:300-5000
    限制
    仅限研究用
  • 状态
    Liquid
    浓度
    1 μg/μL
    缓冲液
    Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
    储存液
    ProClin
    注意事项
    This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
    储存条件
    -20 °C
    储存方法
    Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
    有效期
    12 months
  • 抗原
    MCCC2 (Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
    别名
    MCCC2 (MCCC2 产品)
    别名
    si:dkey-57m14.1 antibody, zgc:85685 antibody, MCCB antibody, 3-METHYLCROTONYL-COA CARBOXYLASE antibody, 3-methylcrotonyl-CoA carboxylase antibody, F28A23.210 antibody, F28A23_210 antibody, 4930552N12Rik antibody, methylcrotonoyl-CoA carboxylase 2 (beta) antibody, methylcrotonoyl-CoA carboxylase 2 antibody, methylcrotonoyl-CoA carboxylase 2 S homeolog antibody, 3-methylcrotonyl-CoA carboxylase antibody, methylcrotonoyl-Coenzyme A carboxylase 2 (beta) antibody, mccc2 antibody, MCCC2 antibody, mccc2.S antibody, Mccc2 antibody, MCCB antibody
    背景

    Synonyms: 3 methylcrotonyl CoA carboxylase 2, 3 methylcrotonyl CoA carboxylase non biotin containing subunit, 3 methylcrotonyl CoA:carbon dioxide ligase subunit beta, 3-methylcrotonyl-CoA carboxylase 2, 3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit, 3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta, Biotin carboxylase, MCCase subunit beta, MCCB, MCCB_HUMAN, MCCC 2, Mccc2, Methylcrotonoyl CoA carboxylase 2 (beta), Methylcrotonoyl CoA carboxylase beta chain mitochondrial, Methylcrotonoyl Coenzyme A carboxylase 2 (beta), Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial, Non biotin containing subunit of 3 methylcrotonyl CoA carboxylase.

    Background: This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.

    基因ID
    64087
    UniProt
    Q9HCC0
You are here:
客服