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HADHA 抗体
HADHA
适用: 人, 小鼠
WB, IHC, IF, ELISA
宿主: 兔
Polyclonal
unconjugated
HADHA抗体详情
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抗原
See all HADHA 抗体
HADHA
(Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))
适用
All reactivities for HADHA 抗体
人, 小鼠
宿主
All hosts for HADHA 抗体
兔
克隆类型
All clonalities for HADHA 抗体
多克隆
标记
All conjugates for HADHA 抗体
This HADHA antibody is un-conjugated
应用范围
All applications for HADHA 抗体
Western Blotting (WB), Immunohistochemistry (IHC), Immunofluorescence (IF), ELISA
纯化方法
Immunogen affinity purified
纯度
≥95 % as determined by SDS-PAGE
免疫原
hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), alpha subunit
亚型
IgG
Top Product
Discover our top product HADHA Primary Antibody
Alternatives
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使用细节
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应用备注
WB: 1:500 - 1:2000, IHC: 1:50 - 1:200, IF: 1:50 - 1:200
限制
仅限研究用
贮存及处理
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状态
Liquid
缓冲液
PBS with 0.02 % sodium azide and 50 % glycerol pH 7.3 ,
储存液
Sodium azide
注意事项
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
储存条件
-20 °C
储存方法
-20°C for 12 months (Avoid repeated freeze / thaw cycles.)
有效期
12 months
HADHA目标详情
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抗原
HADHA
(Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))
别名
HADHA (HADHA 产品 )
别名
cb1055 antibody, hadha antibody, im:7136067 antibody, wu:fa14c08 antibody, ECHA antibody, GBP antibody, HADH antibody, LCEH antibody, LCHAD antibody, MTPA antibody, TP-ALPHA antibody, RGD1560655 antibody, C77020 antibody, Mtpa antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha antibody, hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha S homeolog antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha a antibody, hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), alpha subunit antibody, HADHA antibody, hadha antibody, hadha.S antibody, hadhaa antibody, Hadha antibody
背景
Synonyms:HADH Background:This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.
分子量
88 kDa
基因ID
3030
UniProt
P40939
途径
Monocarboxylic Acid Catabolic Process
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