HADHA 抗体 (AA 484-763)
-
- 抗原 See all HADHA 抗体
- HADHA (Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))
-
抗原表位
- AA 484-763
-
适用
- 人
-
宿主
- 兔
-
克隆类型
- 多克隆
-
标记
- This HADHA antibody is un-conjugated
-
应用范围
- Western Blotting (WB), Immunofluorescence (IF), Immunoprecipitation (IP)
- 序列
- IAAVSKRPEK VIGMHYFSPV DKMQLLEIIT TEKTSKDTSA SAVAVGLKQG KVIIVVKDGP GFYTTRCLAP MMSEVIRILQ EGVDPKKLDS LTTSFGFPVG AATLVDEVGV DVAKHVAEDL GKVFGERFGG GNPELLTQMV SKGFLGRKSG KGFYIYQEGV KRKDLNSDMD SILASLKLPP KSEVSSDEDI QFRLVTRFVN EAVMCLQEGI LATPAEGDIG AVFGLGFPPC LGGPFRFVDL YGAQKIVDRL KKYEAAYGKQ FTPCQLLADH ANSPNKKFYQ
- 交叉反应
- 人, 小鼠, 大鼠
- 产品特性
- Polyclonal Antibodies
- 纯化方法
- Affinity purification
- 免疫原
- Recombinant fusion protein containing a sequence corresponding to amino acids 484-763 of human HADHA (NP_000173.2).
- 亚型
- IgG
- Top Product
- Discover our top product HADHA Primary Antibody
-
-
- 应用备注
- WB,1:500 - 1:2000,IF,1:50 - 1:200,IP,1:50 - 1:100
- 说明
-
HIGH QUALITY
- 限制
- 仅限研究用
-
- 状态
- Liquid
- 缓冲液
- PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
-
- 抗原
- HADHA (Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))
- 别名
- HADHA (HADHA 产品)
- 别名
- cb1055 antibody, hadha antibody, im:7136067 antibody, wu:fa14c08 antibody, ECHA antibody, GBP antibody, HADH antibody, LCEH antibody, LCHAD antibody, MTPA antibody, TP-ALPHA antibody, RGD1560655 antibody, C77020 antibody, Mtpa antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha antibody, hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha S homeolog antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha a antibody, hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), alpha subunit antibody, HADHA antibody, hadha antibody, hadha.S antibody, hadhaa antibody, Hadha antibody
- 背景
- This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.,HADHA,ECHA,GBP,HADH,LCEH,LCHAD,MTPA,TP-ALPHA,Cancer,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,Lipid Metabolism,Cardiovascular,Lipids,Fatty Acids,HADHA
- 分子量
- 28 kDa/83 kDa
- 基因ID
- 3030
- UniProt
- P40939
- 途径
- Monocarboxylic Acid Catabolic Process
-