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Dystrophin 抗体
DMD
适用: 小鼠, 大鼠
IHC, IF
宿主: 兔
Polyclonal
unconjugated
Dystrophin抗体详情
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抗原
See all Dystrophin (DMD) 抗体
Dystrophin (DMD)
适用
All reactivities for Dystrophin 抗体
小鼠, 大鼠
宿主
All hosts for Dystrophin 抗体
兔
克隆类型
All clonalities for Dystrophin 抗体
多克隆
标记
All conjugates for Dystrophin 抗体
This Dystrophin antibody is un-conjugated
应用范围
All applications for Dystrophin 抗体
Immunohistochemistry (IHC), Immunofluorescence (IF)
交叉反应
大鼠
纯化方法
Affinity purification
免疫原
Recombinant protein corresponding to Mouse Dystrophin
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Discover our top product DMD Primary Antibody
Alternatives
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使用细节
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应用备注
IHC/IF (M,R) 1:600-1:1200
限制
仅限研究用
贮存及处理
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状态
Liquid
缓冲液
PBS, pH 7.4, 0.02 % sodium azide
储存液
Sodium azide
注意事项
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
储存条件
-20 °C
Dystrophin目标详情
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抗原
Dystrophin (DMD)
别名
Dystrophin (DMD 产品 )
别名
DMD antibody, Dmd antibody, MGC83347 antibody, DKFZp459C1629 antibody, dmd antibody, MGC79631 antibody, DKFZp468A1620 antibody, Dp71 antibody, cb664 antibody, zfDYS antibody, im:6911785 antibody, zgc:110165 antibody, BMD antibody, CMD3B antibody, DXS142 antibody, DXS164 antibody, DXS206 antibody, DXS230 antibody, DXS239 antibody, DXS268 antibody, DXS269 antibody, DXS270 antibody, DXS272 antibody, DXSmh7 antibody, DXSmh9 antibody, Dp427 antibody, dys antibody, mdx antibody, pke antibody, DNADMD1 antibody, RATDMD antibody, CG17750 antibody, CG31175 antibody, CG34157 antibody, CG7240 antibody, CG7243 antibody, CG7344 antibody, DLP antibody, DLP1 antibody, DLP186 antibody, DLP2 antibody, DLP3 antibody, DmDLP antibody, DmDYS antibody, Dmel\\CG34157 antibody, Dp117 antibody, Dp186 antibody, Dp205 antibody, GI3046716 antibody, IDLP antibody, det antibody, dmDLP antibody, dmDp186 antibody, dmDys antibody, dystrophin antibody, dystrophin, gene 1 L homeolog antibody, dystrophin, gene 1 antibody, dystrophin, muscular dystrophy antibody, Dystrophin antibody, DMD antibody, LOC708073 antibody, dmd.1.L antibody, LOC465557 antibody, dmd.1 antibody, dmd antibody, Dmd antibody, Dys antibody
背景
Dystrophin (DMD or BMD) is a large muscle protein whose mutations cause Duchenne muscular dystrophy (DMD) and Becker muscular dystrophy (BMD), the childhood neuromuscular disorders that result in progressive muscle weakness, respiratory difficulties and cardiovascular dysfunction. Dystrophin is a crucial component of the dystrophin-glycoprotein complex which is essential for muscle membrane integrity and stability. Dystrophin is located on the cytoplasmic face of the sarcolemma and connects the cytoskeletal network to the sarcolemma and extracellular matrix. Multiple isoforms of dystrophin exist due to the alternative splicing, with a wide range of MW (69-72, 110-143, 271, 426 kDa). Most tissues contain transcripts of several isoforms.
基因ID
13405
NCBI登录号
NP_031894
UniProt
P11531
途径
Skeletal Muscle Fiber Development
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