×
我们推荐在您的浏览器上开启Javascript,以获得最佳效果。
MCCC1 抗体 (AA 526-725)
MCCC1
适用: 人
WB, IHC
宿主: 兔
Polyclonal
unconjugated
MCCC1抗体详情
(hide)
抗原
See all MCCC1 抗体
MCCC1
(Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1))
抗原表位
All epitopes for MCCC1 抗体
AA 526-725
适用
All reactivities for MCCC1 抗体
人
宿主
All hosts for MCCC1 抗体
兔
克隆类型
All clonalities for MCCC1 抗体
多克隆
标记
All conjugates for MCCC1 抗体
This MCCC1 antibody is un-conjugated
应用范围
All applications for MCCC1 抗体
Western Blotting (WB), Immunohistochemistry (IHC)
序列
FTLQAHDQFS PFSSSSGRRL NISYTRNMTL KDGKNNVAIA VTYNHDGSYS MQIEDKTFQV LGNLYSEGDC TYLKCSVNGV ASKAKLIILE NTIYLFSKEG SIEIDIPVPK YLSSVSSQET QGGPLAPMTG TIEKVFVKAG DKVKAGDSLM VMIAMKMEHT IKSPKDGTVK KVFYREGAQA NRHTPLVEFE EEESDKRESE
交叉反应
人, 小鼠
产品特性
Polyclonal Antibodies
免疫原
Recombinant fusion protein containing a sequence corresponding to amino acids 526-725 of human MCCC1 (NP_064551.3).
亚型
IgG
Top Product
Discover our top product MCCC1 Primary Antibody
Alternatives
(show)
使用细节
(hide)
应用备注
WB,1:500 - 1:1000,IHC,1:50 - 1:100
限制
仅限研究用
贮存及处理
(hide)
状态
Liquid
缓冲液
PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
储存液
Sodium azide
注意事项
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
储存条件
-20 °C
储存方法
Store at -20°C. Avoid freeze / thaw cycles.
MCCC1目标详情
(hide)
抗原
MCCC1
(Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1))
别名
MCCC1 (MCCC1 产品 )
别名
MCC-B antibody, MCCA antibody, 1810045E08Rik antibody, 2310058B18Rik antibody, MCCalpha antibody, Mcca antibody, R75106 antibody, methylcrotonoyl-CoA carboxylase 1 antibody, methylcrotonyl-CoA carboxylase alpha chain antibody, methylcrotonoyl-Coenzyme A carboxylase 1 (alpha) antibody, MCCC1 antibody, Mccc1 antibody, MCCA antibody
背景
This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.,MCCC1,MCC-B,MCCA,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,Amino acid metabolism,MCCC1
分子量
80 kDa
基因ID
56922
UniProt
Q96RQ3
Recently viewed
(hide)