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MCCC1 抗体 (AA 526-725)

MCCC1 适用: 人 WB, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6143628
发货至: 中国
  • 抗原 See all MCCC1 抗体
    MCCC1 (Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1))
    抗原表位
    • 7
    • 6
    • 6
    • 6
    • 4
    • 3
    • 2
    • 2
    • 1
    • 1
    • 1
    AA 526-725
    适用
    • 37
    • 20
    • 2
    • 1
    • 1
    • 1
    • 1
    宿主
    • 32
    • 6
    克隆类型
    • 35
    • 3
    多克隆
    标记
    • 15
    • 7
    • 3
    • 3
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    This MCCC1 antibody is un-conjugated
    应用范围
    • 26
    • 23
    • 5
    • 1
    • 1
    • 1
    Western Blotting (WB), Immunohistochemistry (IHC)
    序列
    FTLQAHDQFS PFSSSSGRRL NISYTRNMTL KDGKNNVAIA VTYNHDGSYS MQIEDKTFQV LGNLYSEGDC TYLKCSVNGV ASKAKLIILE NTIYLFSKEG SIEIDIPVPK YLSSVSSQET QGGPLAPMTG TIEKVFVKAG DKVKAGDSLM VMIAMKMEHT IKSPKDGTVK KVFYREGAQA NRHTPLVEFE EEESDKRESE
    交叉反应
    人, 小鼠
    产品特性
    Polyclonal Antibodies
    免疫原
    Recombinant fusion protein containing a sequence corresponding to amino acids 526-725 of human MCCC1 (NP_064551.3).
    亚型
    IgG
    Top Product
    Discover our top product MCCC1 Primary Antibody
  • 应用备注
    WB,1:500 - 1:1000,IHC,1:50 - 1:100
    限制
    仅限研究用
  • 状态
    Liquid
    缓冲液
    PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
    储存液
    Sodium azide
    注意事项
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    储存条件
    -20 °C
    储存方法
    Store at -20°C. Avoid freeze / thaw cycles.
  • 抗原
    MCCC1 (Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1))
    别名
    MCCC1 (MCCC1 产品)
    别名
    MCC-B antibody, MCCA antibody, 1810045E08Rik antibody, 2310058B18Rik antibody, MCCalpha antibody, Mcca antibody, R75106 antibody, methylcrotonoyl-CoA carboxylase 1 antibody, methylcrotonyl-CoA carboxylase alpha chain antibody, methylcrotonoyl-Coenzyme A carboxylase 1 (alpha) antibody, MCCC1 antibody, Mccc1 antibody, MCCA antibody
    背景
    This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.,MCCC1,MCC-B,MCCA,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,Amino acid metabolism,MCCC1
    分子量
    80 kDa
    基因ID
    56922
    UniProt
    Q96RQ3
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