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MCCC1 产品

(Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1))

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This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. [provided by RefSeq, Jul 2008].

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Featured MCCC1 Categories

MCCC1 抗体

High quality antibodies with extensive validation data.

MCCC1 ELISA试剂盒

Reliable ELISA kits for a wide range of species.

MCCC1 蛋白

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended MCCC1 抗体

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application ELISA, IHC, IP
Validations
  • (3)
Cat. No. ABIN7159631
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, ELISA, IHC
Validations
  • (2)
Cat. No. ABIN7159632
Quantity 100 μL
Datasheet Datasheet
Reactivity Human, Mouse
Application WB, ELISA, IHC
Validations
  • (2)
Cat. No. ABIN7252978
Quantity 200 μL
Datasheet Datasheet

Recommended MCCC1 ELISA试剂盒

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
Cat. No. ABIN6975007
Quantity 96 tests
Datasheet Datasheet

Recommended MCCC1 蛋白

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1310527
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1310529
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Insect Cells
Validations
  • (1)
Cat. No. ABIN3083526
Quantity 1 mg
Datasheet Datasheet

Latest Publications for our MCCC1 Products

Ingaramo, Beckett: "Selectivity in post-translational biotin addition to five human carboxylases." in: The Journal of biological chemistry, Vol. 287, Issue 3, pp. 1813-22, (2012) (PubMed).

Synonyms and alternative names related to MCCC1

methylcrotonoyl-CoA carboxylase 1 (MCCC1), methylcrotonoyl-CoA carboxylase 1 (Mccc1), methylcrotonyl-CoA carboxylase alpha chain (MCCA), methylcrotonoyl-Coenzyme A carboxylase 1 (alpha) (Mccc1), 1810045E08Rik, 2310058B18Rik, MCC-B, MCCA, Mcca, MCCalpha, R75106

Protein level used designations for MCCC1

  • 3-methylcrotonyl-CoA carboxylase 1
  • 3-methylcrotonyl-CoA carboxylase biotin-containing subunit
  • 3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha
  • MCCase subunit alpha
  • methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
  • methylcrotonoyl-Coenzyme A carboxylase 1 (alpha)
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