PEX1 产品
(Peroxisomal Biogenesis Factor 1 (PEX1))
Categories
This gene encodes a member of the AAA ATPase family, a large group of ATPases associated with diverse cellular activities. This protein is cytoplasmic but is often anchored to a peroxisomal membrane where it forms a heteromeric complex and plays a role in the import of proteins into peroxisomes and peroxisome biogenesis. Mutations in this gene have been associated with complementation group 1 peroxisomal disorders such as neonatal adrenoleukodystrophy, infantile Refsum disease, and Zellweger syndrome. [provided by RefSeq, Jul 2008].
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Featured PEX1 Categories
Recommended PEX1 抗体
Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity
Human
Application
ELISA, IHC, IF
Validations
- (2)
Cat. No.
ABIN7163001
Quantity
100 μg
Datasheet
Datasheet
Reactivity
Human
Application
WB, IHC, ICC
Validations
- (3)
Cat. No.
ABIN5014081
Quantity
100 μL
Datasheet
Datasheet
Reactivity
Mouse
Application
WB, IHC, ICC
Validations
- (3)
Cat. No.
ABIN5014080
Quantity
100 μL
Datasheet
Datasheet
Recommended PEX1 ELISA试剂盒
Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity
Human
Analytical Method
Sandwich ELISA
Validations
Cat. No.
ABIN418397
Quantity
96 tests
Datasheet
Datasheet
Recommended PEX1 蛋白
Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity
Human
Source
Tobacco (Nicotiana tabacum)
Validations
- (1)
Cat. No.
ABIN3094488
Quantity
1 mg
Datasheet
Datasheet
Reactivity
Mouse
Source
Tobacco (Nicotiana tabacum)
Validations
- (1)
Cat. No.
ABIN3135168
Quantity
1 mg
Datasheet
Datasheet
Reactivity
Human
Source
Escherichia coli (E. coli)
Validations
Cat. No.
ABIN7419214
Quantity
100 μg
Datasheet
Datasheet
Latest Publications for our PEX1 Products
: "Peroxisomal monoubiquitinated PEX5 interacts with the AAA ATPases PEX1 and PEX6 and is unfolded during its dislocation into the cytosol." in: The Journal of biological chemistry, Vol. 293, Issue 29, pp. 11553-11563, (2019) (PubMed).: "Identification of novel mutations and sequence variation in the Zellweger syndrome spectrum of peroxisome biogenesis disorders." in: Human mutation, Vol. 30, Issue 3, pp. E467-80, (2009) (PubMed).
: "Identification of a common PEX1 mutation in Zellweger syndrome." in: Human mutation, Vol. 14, Issue 1, pp. 45-53, (1999) (PubMed).
: "Disruption of a PEX1-PEX6 interaction is the most common cause of the neurologic disorders Zellweger syndrome, neonatal adrenoleukodystrophy, and infantile Refsum disease." in: Proceedings of the National Academy of Sciences of the United States of America, Vol. 95, Issue 15, pp. 8630-5, (1998) (PubMed).
: "Mutations in PEX1 are the most common cause of peroxisome biogenesis disorders." in: Nature genetics, Vol. 17, Issue 4, pp. 445-8, (1997) (PubMed).
Synonyms and alternative names related to PEX1
peroxisomal biogenesis factor 1 (PEX1), peroxisomal biogenesis factor 1 (Pex1), peroxisomal biogenesis factor 1 L homeolog (pex1.L), 5430414H02Rik, E330005K07Rik, PBD1A, PBD1B, pex1, RGD1559939, ZWS, ZWS1Protein level used designations for PEX1
- Zellweger syndrome
- peroxin-1
- peroxisome biogenesis disorder protein 1
- peroxisome biogenesis factor 1
- peroxisomal biogenesis factor 1 L homeolog
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