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Complement Factor I 抗体

(Complement Factor I (CFI))
This gene encodes a serine proteinase that is essential for regulating the complement cascade. The encoded preproprotein is cleaved to produce both heavy and light chains, which are linked by disulfide bonds to form a heterodimeric glycoprotein. This heterodimer can cleave and inactivate the complement components C4b and C3b, and it prevents the assembly of the C3 and C5 convertase enzymes. Defects in this gene cause complement factor I deficiency, an autosomal recessive disease associated with a susceptibility to pyogenic infections. Mutations in this gene have been associated with a predisposition to atypical hemolytic uraemic syndrome, a disease characterized by acute renal failure, microangiopathic hemolytic anemia and thrombocytopenia. Primary glomerulonephritis with immmune deposits is another condition associated with mutation of this gene. [provided by RefSeq, Jul 2008].

57 results

CFI 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7444067
 
CFI 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7443707
 
CFI 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 1B3 unconjugated
产品编号 ABIN516816
 
CFI 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7148403
 
CFI 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN516814
 
CFI 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7434455
 
CFI 适用: 人 WB, ELISA 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN561424
 
CFI 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6748298
 
CFI 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN516815
 
CFI 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6138461
 
CFI 适用: 人 EIA, RIA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1803648
 
CFI 适用: 人 EIA, RIA 宿主: 兔 Polyclonal Biotin
产品编号 ABIN1803649
 
CFI 适用: 人, 大鼠 WB, FACS 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN4955823
 
CFI 适用: 人 ELISA 宿主: 兔 Polyclonal HRP
产品编号 ABIN7148406
 
CFI 适用: 人 宿主: 兔 Polyclonal FITC
产品编号 ABIN7148405
 
CFI 适用: 人 ELISA 宿主: 兔 Polyclonal Biotin
产品编号 ABIN7148404
 
CFI 适用: 人 WB, IHC, IP, ICC 宿主: 小鼠 Monoclonal unconjugated
产品编号 ABIN7637374
 
CFI 适用: 人 WB, ELISA, IP, FACS, RIA 宿主: 小鼠 Monoclonal OX-21 Biotin
产品编号 ABIN308056
 
CFI 适用: 人 FACS 宿主: 小鼠 Monoclonal OX-21 FITC
产品编号 ABIN308057
 
CFI 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7568826
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • Immunohistochemistry (IHC)
    • ELISA
    • Immunoprecipitation (IP)
    • Flow Cytometry (FACS)
    • Immunocytochemistry (ICC)
    • Radioimmunoassay (RIA)
    • Enzyme Immunoassay (EIA)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunofluorescence (IF)
    • Functional Studies (Func)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Immunofluorescence (fixed cells) (IF/ICC)
  • 适用
    • Human
    • Mouse
    • Rat
    • Cow
    • Dog
    • Guinea Pig
    • Horse
    • Monkey
    • Pig
    • Rabbit
  • 图像
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
    • Chimeric
  • 克隆
    • OX-21
    • 17C5
    • 1B3
    • 3R-8
    • 4E9
    • 4H9
    • KT22
  • 抗原表位
    • AA 239-316
    • AA 340-583
    • AA 1-377
    • AA 19-118
    • AA 28-243
    • AA 358-603
    • AA 145-194
    • AA 19-220
    • AA 19-300
    • AA 19-335
    • AA 441-490
    • AA 492-537
    • AA 511-560
    • C-Term
    • N-Term
  • 标记
    • 非结合性
    • FITC
    • Biotin
    • APC
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • HRP
    • PE
    • PerCP
  • 抗体亚型
    • IgG
    • IgG1
    • IgG2b
    • IgG kappa
    • IgG1 kappa
    • IgG2a
  • 蛋白类型
    • Recombinant Antibody
  • Format
    • Liquid
    • Lyophilized
  • Supplier
    • antibodies-online
    • Assaypro
    • Signalway
    • Acris
    • Biomatik
    • Abbexa
    • Aviva Systems Biology
    • Assay Biotechnology Company, Inc.
    • Boster Bio
    • NSJ Bioreagents
    • ProSci

Latest Publications for our Complement Factor I 抗体

Kavanagh, Kemp, Mayland, Winney, Duffield, Warwick, Richards, Ward, Goodship, Goodship: "Mutations in complement factor I predispose to development of atypical hemolytic uremic syndrome." in: Journal of the American Society of Nephrology : JASN, Vol. 16, Issue 7, pp. 2150-5, (2005) (PubMed).

Dragon-Durey, Frémeaux-Bacchi: "Atypical haemolytic uraemic syndrome and mutations in complement regulator genes." in: Springer seminars in immunopathology, Vol. 27, Issue 3, pp. 359-74, (2005) (PubMed).

Crook, Hunt: "Enrichment of early fetal-liver hemopoietic stem cells of the rat using monoclonal antibodies against the transferrin receptor, Thy-1, and MRC-OX82." in: Developmental immunology, Vol. 4, Issue 4, pp. 235-46, (1996) (PubMed).

Aliases for Complement Factor I 抗体

complement factor I S homeolog (cfi.S) 抗体
complement factor I L homeolog (cfi.L) 抗体
complement factor I (CFI) 抗体
complement factor I (cfi) 抗体
complement component factor i (Cfi) 抗体
complement factor I (Cfi) 抗体
ahus3 抗体
AHUS3 抗体
c3b-ina 抗体
C3b-INA 抗体
c3bc4bi 抗体
c3bina 抗体
C3BINA 抗体
cfi 抗体
Cfi 抗体
CFI 抗体
factor I 抗体
FI 抗体
gb:ai721528 抗体
IF 抗体
kaf 抗体
KAF 抗体
MGC53615 抗体
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