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BCKDHB 抗体 (N-Term)

BCKDHB 适用: 人 WB, FACS, IF, IHC (p), EIA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN950620
发货至: 中国
  • 抗原 See all BCKDHB 抗体
    BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
    抗原表位
    • 8
    • 8
    • 6
    • 1
    • 1
    AA 44-74, N-Term
    适用
    • 18
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    宿主
    • 18
    克隆类型
    • 18
    多克隆
    标记
    • 8
    • 2
    • 2
    • 2
    • 2
    • 2
    This BCKDHB antibody is un-conjugated
    应用范围
    • 18
    • 14
    • 13
    • 13
    • 13
    • 5
    • 2
    Western Blotting (WB), Flow Cytometry (FACS), Immunofluorescence (IF), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Enzyme Immunoassay (EIA)
    特异性
    This antibody reacts to BCKDHB.
    交叉反应 (详细)
    Species reactivity (tested):Human.
    纯化方法
    Affinity chromatography on Protein A
    免疫原
    KLH conjugated synthetic peptide between 44-74 amino acids from the N-terminal region of human BCKDHB
    亚型
    Ig Fraction
    Top Product
    Discover our top product BCKDHB Primary Antibody
  • 应用备注
    Optimal working dilution should be determined by the investigator.
    限制
    仅限研究用
  • 状态
    Liquid
    浓度
    0.25 mg/mL
    缓冲液
    PBS containing 0.09 % (W/V) sodium azide as preservative
    储存液
    Sodium azide
    注意事项
    This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    注意事项
    Avoid repeated freezing and thawing.
    储存条件
    4 °C/-20 °C
    储存方法
    Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
  • 抗原
    BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
    别名
    BCKDHB (BCKDHB 产品)
    别名
    zgc:158777 antibody, BCKDHB antibody, E1B antibody, dJ279A18.1 antibody, branched chain keto acid dehydrogenase E1, beta polypeptide antibody, branched chain keto acid dehydrogenase E1 subunit beta antibody, branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog antibody, branched chain ketoacid dehydrogenase E1, beta polypeptide antibody, BCKDHB antibody, bckdhb antibody, bckdhb.S antibody, Bckdhb antibody
    背景
    Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems.Synonyms: 2-oxoisovalerate dehydrogenase subunit beta, alpha-keto acid dehydrogenase, mitochondrial Branched-chain alpha-keto acid dehydrogenase E1 component beta chain
    基因ID
    594
    NCBI登录号
    NP_000047
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