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BCKDHA 抗体 (AA 75-125)

BCKDHA 适用: 人 IP 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7451410
发货至: 中国
  • 抗原 See all BCKDHA 抗体
    BCKDHA (Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA))
    抗原表位
    • 5
    • 4
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    AA 75-125
    适用
    • 22
    • 6
    • 4
    • 3
    • 3
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    宿主
    • 19
    • 3
    克隆类型
    • 21
    • 1
    多克隆
    标记
    • 18
    • 2
    • 1
    • 1
    This BCKDHA antibody is un-conjugated
    应用范围
    • 17
    • 7
    • 4
    • 3
    • 3
    • 2
    • 2
    • 2
    • 1
    Immunoprecipitation (IP)
    原理
    Rabbit anti-BCKDHA Antibody, Affinity Purified
    预测反应
    Chimpanzee
    纯化方法
    Affinity Purified
    免疫原
    Between AA 75 and 125
    亚型
    IgG
    Top Product
    Discover our top product BCKDHA Primary Antibody
  • 应用备注

    IP: 2 - 10 μg/mg lysate

    WB: Not recommended

    限制
    仅限研究用
  • 浓度
    1000 μg/mL
    缓冲液
    Tris-citrate/phosphate buffer, pH 7 to 8 containing 0.09 % Sodium Azide
    储存液
    Sodium azide
    注意事项
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    储存条件
    4 °C
    有效期
    12 months
  • 抗原
    BCKDHA (Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA))
    别名
    BCKDHA (BCKDHA 产品)
    别名
    wu:fd20d04 antibody, zgc:110049 antibody, BCKDE1A antibody, MSU antibody, MSUD1 antibody, OVD1A antibody, BCKDA antibody, E1a antibody, 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial antibody, branched chain keto acid dehydrogenase E1, alpha polypeptide antibody, 2-oxoisovalerate dehydrogenase alpha subunit (branched-chain alpha-keto acid dehydrogenase E1 component alpha chain) (BCKDH E1-alpha) (BCKDE1A) antibody, branched chain ketoacid dehydrogenase E1, alpha polypeptide antibody, LOC704978 antibody, bckdha antibody, BCKDHA antibody, BckdhA antibody, Bckdha antibody
    背景
    Background: BCKDHA (branched chain keto acid dehydrogenase E1, alpha polypeptide) is a component of the branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex. The BCKD complex is an inner mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). Mutations in this gene result in maple syrup urine disease, type IA [taken from NCBI Entrez Gene (Gene ID: 593)].
    基因ID
    593
    NCBI登录号
    NP_000700
    UniProt
    P12694
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