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MMADHC 抗体 (AA 1-296)
MMADHC
适用: 人
WB
宿主: 兔
Polyclonal
unconjugated
MMADHC抗体详情
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抗原
See all MMADHC 抗体
MMADHC
(Methylmalonic Aciduria (Cobalamin Deficiency) CblD Type, with Homocystinuria (MMADHC))
抗原表位
All epitopes for MMADHC 抗体
AA 1-296
适用
All reactivities for MMADHC 抗体
人
宿主
All hosts for MMADHC 抗体
兔
克隆类型
All clonalities for MMADHC 抗体
多克隆
标记
All conjugates for MMADHC 抗体
This MMADHC antibody is un-conjugated
应用范围
All applications for MMADHC 抗体
Western Blotting (WB)
原理
MMADHC Rabbit pAb
序列
MANVLCNRAR LVSYLPGFCS LVKRVVNPKA FSTAGSSGSD ESHVAAAPPD ICSRTVWPDE TMGPFGPQDQ RFQLPGNIGF DCHLNGTASQ KKSLVHKTLP DVLAEPLSSE RHEFVMAQYV NEFQGNDAPV EQEINSAETY FESARVECAI QTCPELLRKD FESLFPEVAN GKLMILTVTQ KTKNDMTVWS EEVEIEREVL LEKFINGAKE ICYALRAEGY WADFIDPSSG LAFFGPYTNN TLFETDERYR HLGFSVDDLG CCKVIRHSLW GTHVVVGSIF TNATPDSHIM KKLSGN
交叉反应
人, 小鼠, 大鼠
产品特性
Polyclonal Antibodies
纯化方法
Affinity purification
免疫原
Recombinant fusion protein containing a sequence corresponding to amino acids 1-296 of human MMADHC (NP_056517.1).
亚型
IgG
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Alternatives
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anti-Methylmalonic Aciduria (Cobalamin Deficiency) CblD Type, with Homocystinuria (MMADHC) (AA 35-84) antibody
MMADHC
适用: 人, 小鼠, 大鼠, Cow, 犬, 山羊, 豚鼠, 马, 兔, 斑马鱼, 小鸡, Hamster, 猴, 非洲爪蟾, Bat
WB
宿主: 兔
Polyclonal
unconjugated
anti-Methylmalonic Aciduria (Cobalamin Deficiency) CblD Type, with Homocystinuria (MMADHC) (AA 216-265) antibody
MMADHC
适用: 人, 小鼠, 大鼠, Cow, 犬, 山羊, 豚鼠, 马, 兔, 小鸡, Hamster, 猴, 非洲爪蟾, Pig
WB
宿主: 兔
Polyclonal
unconjugated
使用细节
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应用备注
WB,1:500 - 1:2000
限制
仅限研究用
贮存及处理
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状态
Liquid
缓冲液
PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
储存液
Sodium azide
注意事项
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
储存条件
-20 °C
储存方法
Store at -20°C. Avoid freeze / thaw cycles.
MMADHC目标详情
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抗原
MMADHC
(Methylmalonic Aciduria (Cobalamin Deficiency) CblD Type, with Homocystinuria (MMADHC))
别名
MMADHC (MMADHC 产品 )
别名
C2orf25 antibody, CL25022 antibody, cblD antibody, 2010311D03Rik antibody, AI314967 antibody, RGD1303272 antibody, methylmalonic aciduria and homocystinuria, cblD type antibody, methylmalonic aciduria (cobalamin deficiency) cblD type, with homocystinuria antibody, MMADHC antibody, Mmadhc antibody
背景
This gene encodes a mitochondrial protein that is involved in an early step of vitamin B12 metabolism. Vitamin B12 (cobalamin) is essential for normal development and survival in humans. Mutations in this gene cause methylmalonic aciduria and homocystinuria type cblD (MMADHC), a disorder of cobalamin metabolism that is characterized by decreased levels of the coenzymes adenosylcobalamin and methylcobalamin. Pseudogenes have been identified on chromosomes 11 and X.,MMADHC,C2orf25,CL25022,cblD,cblD type,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,MMADHC
分子量
32kDa
基因ID
27249
UniProt
Q9H3L0
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