MMACHC 抗体
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- 抗原 See all MMACHC 抗体
- MMACHC (Methylmalonic Aciduria (Cobalamin Deficiency) CblC Type, with Homocystinuria (MMACHC))
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适用
- 人, 小鼠, 大鼠
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This MMACHC antibody is un-conjugated
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应用范围
- Western Blotting (WB)
- 纯化方法
- Affinity purification
- 免疫原
- Recombinant protein of human MMACHC
- 亚型
- IgG
- Top Product
- Discover our top product MMACHC Primary Antibody
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- 应用备注
- WB 1:500 - 1:2000
- 限制
- 仅限研究用
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- 浓度
- 1 mg/mL
- 缓冲液
- Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3.
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- 抗原
- MMACHC (Methylmalonic Aciduria (Cobalamin Deficiency) CblC Type, with Homocystinuria (MMACHC))
- 别名
- MMACHC (MMACHC 产品)
- 别名
- cblC antibody, RP11-291L19.3 antibody, RGD1310806 antibody, 1810037K07Rik antibody, methylmalonic aciduria (cobalamin deficiency) cblC type, with homocystinuria antibody, methylmalonic aciduria cblC type, with homocystinuria antibody, MMACHC antibody, Mmachc antibody
- 背景
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Synonyms: 1810037K07Rik,BOS_3654,cblC,DKFZp564I122,FLJ25671,Methylmalonic aciduria (cobalamin deficiency) cblC type with homocystinuria,Methylmalonic aciduria and homocystinuria type C protein,Methylmalonic aciduria and homocystinuria type C protein homolog,MGC134307,MMAC,MMACHC,OTTHUMP00000009243,RP11 291L19.3,RP23-177C18.3
Background: The exact function of the protein encoded by this gene is not known, however, its C-terminal region shows similarity to TonB, a bacterial protein involved in energy transduction for cobalamin (vitamin B12) uptake. Hence, it is postulated that this protein may have a role in the binding and intracellular trafficking of cobalamin. Mutations in this gene are associated with methylmalonic aciduria and homocystinuria type cblC.
- 分子量
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Observed_MW: 32kDa
Calculated_MW: 31kDa
- 基因ID
- 25974
- UniProt
- Q9Y4U1
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