EHHADH 抗体
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- 抗原 See all EHHADH 抗体
- EHHADH (Enoyl-CoA, Hydratase/3-Hydroxyacyl CoA Dehydrogenase (EHHADH))
- 适用
- 人, 小鼠, 大鼠
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This EHHADH antibody is un-conjugated
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应用范围
- Western Blotting (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)
- 纯化方法
- Affinity purification
- 免疫原
- Recombinant protein of human EHHADH
- 亚型
- IgG
- Top Product
- Discover our top product EHHADH Primary Antibody
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- 应用备注
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WB 1:500 - 1:2000
IHC 1:50 - 1:200
IF 1:50 - 1:200 - 说明
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Liver and kidney, Strongly expressed in the terminal segments of the proximal tubule, Lower amounts seen in the brain
- 限制
- 仅限研究用
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- 缓冲液
- PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3.
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20C. Avoid freeze / thaw cycles.
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- 抗原
- EHHADH (Enoyl-CoA, Hydratase/3-Hydroxyacyl CoA Dehydrogenase (EHHADH))
- 别名
- EHHADH (EHHADH 产品)
- 别名
- ECHD antibody, L-PBE antibody, LBFP antibody, LBP antibody, PBFE antibody, 1 antibody, Lbp antibody, MEF antibody, Mfe antibody, Mfe1 antibody, Pbe antibody, Pbfe antibody, perMFE-1 antibody, 1300002P22Rik antibody, HD antibody, MFP antibody, MFP1 antibody, zgc:77526 antibody, Ehhadh antibody, enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase antibody, enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase antibody, enoyl-Coenzyme A, hydratase/3-hydroxyacyl Coenzyme A dehydrogenase antibody, peroxisomal bifunctional enzyme-like antibody, EHHADH antibody, ehhadh antibody, Ehhadh antibody, LOC100135519 antibody
- 背景
- The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene.
- 分子量
- 79.495 kDa
- 基因ID
- 1962
- UniProt
- Q08426
- 途径
- Monocarboxylic Acid Catabolic Process
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