MMAA 抗体 (AbBy Fluor® 750)
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- 抗原 See all MMAA 抗体
- MMAA (Methylmalonic Aciduria (Cobalamin Deficiency) Type A (MMAA))
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适用
- 人, 小鼠, 大鼠
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This MMAA antibody is conjugated to AbBy Fluor® 750
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应用范围
- Western Blotting (WB), Immunofluorescence (Paraffin-embedded Sections) (IF (p))
- 交叉反应
- 人, 小鼠, 大鼠
- 纯化方法
- Purified by Protein A.
- 免疫原
- KLH conjugated synthetic peptide derived from human MMAA/cblA
- 亚型
- IgG
- Top Product
- Discover our top product MMAA Primary Antibody
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- 应用备注
- IF(IHC-P) 1:50-200
- 限制
- 仅限研究用
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- 状态
- Liquid
- 浓度
- 1 μg/μL
- 缓冲液
- Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
- 储存液
- ProClin
- 注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
- 有效期
- 12 months
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- 抗原
- MMAA (Methylmalonic Aciduria (Cobalamin Deficiency) Type A (MMAA))
- 别名
- cblA (MMAA 产品)
- 别名
- 2810018E08Rik antibody, AI840684 antibody, cblA antibody, methylmalonic aciduria (cobalamin deficiency) type A antibody, methylmalonic aciduria (cobalamin deficiency) cblA type antibody, Mmaa antibody, MMAA antibody
- 背景
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Synonyms: mitochondrial, cblA, MMAA protein, Methylmalonic aciduria cobalamin deficiency cblA type, Methylmalonic aciduria cobalamin deficiency type A, Methylmalonic aciduria type A protein, Methylmalonic aciduria type A protein mitochondrial, MMAA, MMAA_HUMAN.
Background: The protein encoded by this gene is involved in the translocation of cobalamin into the mitochondrion, where it is used in the final steps of adenosylcobalamin synthesis. Adenosylcobalamin is a coenzyme required for the activity of methylmalonyl-CoA mutase. Defects in this gene are a cause of methylmalonic aciduria. [provided by RefSeq, Jul 2008].
- 基因ID
- 166785
- 途径
- Monocarboxylic Acid Catabolic Process
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