CLN6 抗体
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- 抗原 See all CLN6 抗体
- CLN6 (Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6))
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适用
- 人
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This CLN6 antibody is un-conjugated
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应用范围
- Western Blotting (WB), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
- 特异性
- CLN6 antibody detects endogenous levels of CLN6 protein.(region surrounding asn258)
- 纯化方法
- Affinity chromatography
- Top Product
- Discover our top product CLN6 Primary Antibody
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anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) antibody
CLN6 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) (Internal Region) antibodyCLN6 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC, IF, ICC 宿主: 兔 Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) (AA 1-43) antibodyCLN6 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) (C-Term) antibodyCLN6 适用: 人, 小鼠, 大鼠, 犬, 马, 兔, Cow, 绵羊, 斑马鱼, Pig, 猴, Bat WB 宿主: 兔 Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) (AA 108-157) antibodyCLN6 适用: 人, 小鼠, 大鼠, 犬, 马, 豚鼠, 猴, Bat, 小鸡 WB 宿主: 兔 Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) (AA 221-270) antibodyCLN6 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) (C-Term) antibodyCLN6 适用: 人, 小鼠, 大鼠, 犬, 马, 豚鼠, 兔, Cow, 绵羊, 斑马鱼, Pig WB, IHC 宿主: 兔 Polyclonal unconjugated
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- 应用备注
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ELISA: 1: 40000approx. 1: 60000. WB: 1: 500approx. 1: 1000. IHC: 1: 50approx. 1: 200.
Other applications not tested.
Optimal dilutions are dependent on conditions and should be determined by the user. - 限制
- 仅限研究用
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- 浓度
- 1,0 mg/mL
- 缓冲液
- Phosphate buffered saline (PBS) with 0.05 % sodium azide, approx. pH 7.2.
- 储存液
- Sodium azide
- 注意事项
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 注意事项
- Avoid repeated freezing and thawing.
- 储存条件
- 4 °C/-20 °C
- 储存方法
- Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
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- 抗原
- CLN6 (Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6))
- 别名
- CLN6 (CLN6 产品)
- 别名
- 1810065L06Rik antibody, AW743417 antibody, D9Bwg1455e antibody, nclf antibody, CLN4A antibody, HsT18960 antibody, cln6 antibody, zgc:103565 antibody, ceroid-lipofuscinosis, neuronal 6 antibody, CLN6, transmembrane ER protein antibody, CLN6, transmembrane ER protein S homeolog antibody, ceroid-lipofuscinosis, neuronal 6, late infantile, variant antibody, CLN6, transmembrane ER protein a antibody, Cln6 antibody, CLN6 antibody, cln6.S antibody, cln6a antibody
- 背景
- CLN6, a 311-amino acid protein, has 7 predicted transmembrane domains and is conserved across vertebrates. The CLN6 protein localizes to the endoplasmic reticulum but contributes to lysosomal function. Mutations in the CLN6 gene cause variant late-onset infantile neuronal ceroid lipofuscinosis (vLINCL), a lysosomal storage disorder marked by progressive mental deterioration and blindness, part of a group of severe inherited neurodegenerative disorders affecting children wherein lysosomes accumulate storage material, causing the death of neurons. CLN6 is one of eight proteins, including CLN1-8, that are associated with NCL.Synonyms: Ceroid-lipofuscinosis neuronal protein 6
- 分子量
- approx. 40 kDa
- 基因ID
- 54982
- NCBI登录号
- NP_060352
- UniProt
- Q9NWW5
- 途径
- Glycosaminoglycan Metabolic Process
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