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Phenylalanine Hydroxylase 抗体

(Phenylalanine Hydroxylase)
PAH encodes the enzyme phenylalanine hydroxylase that is the rate-limiting step in phenylalanine catabolism. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria. [provided by RefSeq, Jul 2008].

69 results :

适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7438214
 
Verified 适用: 人, 大鼠 WB, ELISA 宿主: 山羊 Polyclonal unconjugated
产品编号 ABIN571236
 
适用: 人, 小鼠, 大鼠 WB, IHC (p) 宿主: 小鼠 Monoclonal 717CT21-1-1 unconjugated
Pubmed 4 references
产品编号 ABIN1944892
 
适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7435124
 
适用: 人 WB, IHC, ELISA, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7163080
 
适用: 人 WB, IHC (p) 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN518596
 
适用: 人, 小鼠, 大鼠 WB, IHC, FACS 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN5518942
 
适用: 人, 小鼠, 大鼠 WB, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7009050
 
适用: 人, 小鼠, 大鼠 WB, IHC, ELISA, ICC, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6264014
 
适用: 人 WB, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN3015513
 
适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7185394
 
适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN518597
 
适用: 人 WB, IHC (p) 宿主: 小鼠 Monoclonal U8Y5 unconjugated
产品编号 ABIN7091525
 
适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6285617
 
适用: 人 宿主: 兔 Polyclonal FITC
产品编号 ABIN7163082
 
适用: 人 ELISA 宿主: 兔 Polyclonal Biotin
产品编号 ABIN7163081
 
适用: 人 ELISA 宿主: 兔 Polyclonal HRP
产品编号 ABIN7163083
 
适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7644234
 
适用: 人 WB, IHC, IP, ICC 宿主: 小鼠 Monoclonal C3 unconjugated
产品编号 ABIN7426547
 
适用: 人 WB, IHC, IP, ICC 宿主: 小鼠 Monoclonal C11 unconjugated
产品编号 ABIN7644236
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • Immunohistochemistry (IHC)
    • ELISA
    • Immunocytochemistry (ICC)
    • Immunoprecipitation (IP)
    • Immunofluorescence (IF)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunofluorescence (fixed cells) (IF/ICC)
    • Flow Cytometry (FACS)
    • Immunochromatography (IC)
  • 适用
    • Human
    • Mouse
    • Rat
  • 论文引用
  • 图像
  • Preservative free only
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
    • Goat
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • C10
    • C11
    • C3
    • C4
    • C7
    • 17D10
    • 17D1017D10
    • 29P62
    • 717CT21-1-1
    • RB24519
    • U8Y5
  • 抗原表位
    • AA 228-452
    • AA 132-161
    • AA 2-452
    • AA 1-226
    • AA 1-452
    • Internal Region
    • AA 140-170
    • C-Term
    • Center
    • AA 1-290
    • AA 103-427
    • AA 121-300
    • AA 127-161
    • AA 351-400
    • AA 71-208
    • Arg400
    • N-Term
  • 标记
    • 非结合性
    • Biotin
    • FITC
    • HRP
    • APC
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • PE
  • 抗体亚型
    • IgG
    • IgG1 kappa
    • IgG2b kappa
    • Ig Fraction
  • 蛋白类型
    • Recombinant Antibody
  • Format
    • Liquid
    • Lyophilized
  • Grade
    • Verified
  • Supplier
    • antibodies-online
    • Biomatik
    • Signalway
    • USBio
    • Abbexa
    • Abcepta
    • Boster Bio
    • Assay Biotechnology Company, Inc.
    • Cloud-Clone

Latest Publications for our Phenylalanine Hydroxylase 抗体

Bonyadi, Omrani, Moghanjoghi, Shiva: "Mutations of the phenylalanine hydroxylase gene in Iranian Azeri Turkish patients with phenylketonuria." in: Genetic testing and molecular biomarkers, Vol. 14, Issue 2, pp. 233-5, (2010) (PubMed).

Siltberg-Liberles, Steen, Svebak, Martinez: "The phylogeny of the aromatic amino acid hydroxylases revisited by characterizing phenylalanine hydroxylase from Dictyostelium discoideum." in: Gene, Vol. 427, Issue 1-2, pp. 86-92, (2008) (PubMed).

Miranda, Teigen, Thórólfsson, Svebak, Knappskog, Flatmark, Martínez: "Phosphorylation and mutations of Ser(16) in human phenylalanine hydroxylase. Kinetic and structural effects." in: The Journal of biological chemistry, Vol. 277, Issue 43, pp. 40937-43, (2002) (PubMed).

Cotton, McAdam, Jennings, Morgan: "A monoclonal antibody to aromatic amino acid hydroxylases. Identification of the epitope." in: The Biochemical journal, Vol. 255, Issue 1, pp. 193-6, (1989) (PubMed).

Kwok, Ledley, DiLella, Robson, Woo: "Nucleotide sequence of a full-length complementary DNA clone and amino acid sequence of human phenylalanine hydroxylase." in: Biochemistry, Vol. 24, Issue 3, pp. 556-61, (1985) (PubMed).

Aliases for Phenylalanine Hydroxylase 抗体

phenylalanine hydroxylase (pah) 抗体
protein henna (LOC408622) 抗体
phenylalanine hydroxylase (PAH) 抗体
phenylalanine hydroxylase (CpipJ_CPIJ002149) 抗体
phenylalanine 4-monooxygenase (pah) 抗体
phenylalanine hydroxylase (Pah) 抗体
AW106920 抗体
cb877 抗体
DDBDRAFT_0206188 抗体
DDBDRAFT_0231664 抗体
DDB_0206188 抗体
DDB_0231664 抗体
GB18494 抗体
PAH 抗体
PH 抗体
phenylalanine-4-hydroxylase 抗体
pku 抗体
PKU 抗体
pku1 抗体
PKU1 抗体
wu:fb02f10 抗体
zgc:65981 抗体
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