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HEXB 产品

(Hexosaminidase B (Beta Polypeptide) (HEXB))

Categories

Hexosaminidase B is the beta subunit of the lysosomal enzyme beta-hexosaminidase that, together with the cofactor GM2 activator protein, catalyzes the degradation of the ganglioside GM2, and other molecules containing terminal N-acetyl hexosamines. Beta-hexosaminidase is composed of two subunits, alpha and beta, which are encoded by separate genes. Both beta-hexosaminidase alpha and beta subunits are members of family 20 of glycosyl hydrolases. Mutations in the alpha or beta subunit genes lead to an accumulation of GM2 ganglioside in neurons and neurodegenerative disorders termed the GM2 gangliosidoses. Beta subunit gene mutations lead to Sandhoff disease (GM2-gangliosidosis type II). [provided by RefSeq, Jul 2008].

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Featured HEXB Categories

HEXB 抗体

High quality antibodies with extensive validation data.

HEXB ELISA试剂盒

Reliable ELISA kits for a wide range of species.

HEXB 蛋白

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended HEXB 抗体

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, IHC, IP, ICC
Validations
  • (7)
Cat. No. ABIN7432289
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, IHC, IP, ICC
Validations
  • (12)
Cat. No. ABIN7438553
Quantity 100 μL
Datasheet Datasheet
Reactivity Mouse
Application WB, IHC, IP, ICC
Validations
  • (9)
Cat. No. ABIN7438139
Quantity 100 μL
Datasheet Datasheet

Recommended HEXB ELISA试剂盒

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (5)
Cat. No. ABIN6574183
Quantity 96 tests
Datasheet Datasheet
Reactivity Mouse
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
  • (1)
Cat. No. ABIN6956521
Quantity 96 tests
Datasheet Datasheet
Reactivity Rat
Analytical Method Quantitative Sandwich ELISA
Validations
  • (2)
  • (1)
Cat. No. ABIN6956522
Quantity 96 tests
Datasheet Datasheet

Recommended HEXB 蛋白

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1306561
Quantity 10 μg
Datasheet Datasheet
Reactivity Mouse
Source HEK-293 Cells
Validations
  • (1)
Cat. No. ABIN7320023
Quantity 100 μg
Datasheet Datasheet
Reactivity Human
Source Escherichia coli (E. coli)
Validations
  • (1)
Cat. No. ABIN3081414
Quantity 1 mg
Datasheet Datasheet

Latest Publications for our HEXB Products

Wu, Chan, Shi, Jhong: "Uncovering the Molecular Mechanism of Anti-Allergic Activity of Silkworm Pupa-Grown Cordyceps militaris Fruit Body." in: The American journal of Chinese medicine, Vol. 45, Issue 3, pp. 497-513, (2017) (PubMed).

Huang, Zhao, Hu, Han, Wang, Yang, Xu, Li, Yao, Chen: "Resveratrol efficiently improves pulmonary function via stabilizing mast cells in a rat intestinal injury model." in: Life sciences, Vol. 185, pp. 30-37, (2017) (PubMed).

Synonyms and alternative names related to HEXB

hexosaminidase B (Hexb), hexosaminidase subunit beta (Hexb), hexosaminidase subunit beta (HEXB), ENC-1AS

Protein level used designations for HEXB

  • N-acetyl-beta-glucosaminidase subunit beta
  • beta-N-acetylhexosaminidase subunit beta
  • beta-hexosaminidase subunit beta
  • hexosaminidase subunit B
  • HCC-7
  • cervical cancer proto-oncogene 7 protein
  • beta-N-acetylhexosaminidase beta subunit
  • beta-hexosaminidase beta subunit
  • 65 kDa epididymal boar protein
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