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GAA 抗体
(Glucosidase, Alpha, Acid (GAA))
This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene. [provided by RefSeq, Jul 2008].
Recommended next Filters:
GAA
适用: 小鼠
WB, IHC, IP, ICC
宿主: 兔
Polyclonal
unconjugated
产品编号 ABIN7439087
100 μL
(More quantities available)
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GAA
适用: 人
WB, IHC, IP, ICC
宿主: 兔
Polyclonal
unconjugated
产品编号 ABIN7431263
100 μL
(More quantities available)
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GAA
适用: 人
WB, IHC, ELISA, IF
宿主: 兔
Polyclonal
unconjugated
产品编号 ABIN7158768
100 μg
(More quantities available)
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GAA
适用: 人
WB, IHC, IHC (p)
宿主: 兔
Polyclonal
RB18979
unconjugated
产品编号 ABIN656475
400 μL
(More quantities available)
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GAA
适用: 人
WB, ELISA
宿主: 小鼠
Monoclonal
3C6
unconjugated
2 references
GAA
适用: 人
WB, IHC, IHC (p)
宿主: 兔
Polyclonal
unconjugated
GAA
适用: 人
WB
宿主: 兔
Polyclonal
unconjugated
GAA
适用: 人
WB, IHC
宿主: 兔
Polyclonal
unconjugated
GAA
适用: 人, 小鼠, 大鼠
WB, ICC, ELISA, IF (cc), IF (p), IHC (p), IHC (fro)
宿主: 兔
Polyclonal
unconjugated
GAA
适用: 大鼠
WB, IHC, IP, ICC
宿主: 兔
Polyclonal
unconjugated
产品编号 ABIN7444157
100 μL
(More quantities available)
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GAA
适用: 人
WB, IP, IF
宿主: 兔
Polyclonal
unconjugated
产品编号 ABIN6140865
100 μL
(More quantities available)
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GAA
适用: 人, 小鼠, 大鼠, Cow, 犬, 豚鼠, 斑马鱼, Hamster, 猴, Pig
WB
宿主: 兔
Polyclonal
unconjugated
GAA
适用: 人
WB
宿主: 小鼠
Polyclonal
unconjugated
GAA
适用: 人
WB, IHC, IP, ICC
宿主: 兔
Polyclonal
unconjugated
产品编号 ABIN1858935
100 μL
(More quantities available)
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GAA
适用: 大鼠
WB, IHC, IP, ICC
宿主: 兔
Polyclonal
unconjugated
产品编号 ABIN1858937
100 μL
(More quantities available)
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GAA
适用: 小鼠
WB, IHC, IP, ICC
宿主: 兔
Polyclonal
unconjugated
产品编号 ABIN1868081
100 μL
(More quantities available)
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GAA
适用: 人, 大鼠
WB, IHC (p)
宿主: 兔
Polyclonal
unconjugated
GAA
适用: 人, 小鼠, 大鼠, Cow, 犬, 豚鼠, 斑马鱼, 马, 兔
WB, IHC
宿主: 兔
Polyclonal
unconjugated
产品编号 ABIN2781771
100 μL
(More quantities available)
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GAA
适用: 人, 小鼠, 大鼠
WB, IF (cc), IF (p)
宿主: 兔
Polyclonal
AbBy Fluor® 750
GAA
适用: 人, 小鼠, 大鼠
WB, IF (cc), IF (p)
宿主: 兔
Polyclonal
AbBy Fluor® 680
Target information, Synonyms, Latest references