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GAA 抗体

(Glucosidase, Alpha, Acid (GAA))
This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene. [provided by RefSeq, Jul 2008].

61 results

GAA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7431263
 
GAA 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7439087
 
GAA 适用: 人 WB, IHC, ELISA, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7158768
 
GAA 适用: 人 WB, IHC, IHC (p) 宿主: 兔 Polyclonal RB18979 unconjugated
产品编号 ABIN656475
 
GAA 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 3C6 unconjugated
Pubmed 2 references
产品编号 ABIN560974
 
GAA 适用: 人 WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1897035
 
GAA 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN515881
 
GAA 适用: 人 WB, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN4886596
 
GAA 适用: 人, 小鼠, 大鼠 WB, ELISA, ICC, IF (cc), IF (p), IHC (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1714619
 
GAA 适用: 大鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7444157
 
GAA 适用: 人, 小鼠, 大鼠, Cow, 犬, 豚鼠, 斑马鱼, Hamster, 猴, Pig WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6738115
 
GAA 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN515880
 
GAA 适用: 人 WB, IP, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6140865
 
GAA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1858935
 
GAA 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1868081
 
GAA 适用: 大鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1858937
 
GAA 适用: 人, 小鼠, 大鼠, Cow, 犬, 豚鼠, 斑马鱼, 马, 兔 WB, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2781771
 
GAA 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC (p), IHC (fro) 宿主: 兔 Polyclonal Biotin
产品编号 ABIN1701117
 
GAA 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 750
产品编号 ABIN5003036
 
GAA 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 680
产品编号 ABIN5003035
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • Immunohistochemistry (IHC)
    • Immunocytochemistry (ICC)
    • Immunoprecipitation (IP)
    • ELISA
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunofluorescence (IF)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Immunofluorescence (fixed cells) (IF/ICC)
    • Flow Cytometry (FACS)
  • 适用
    • Human
    • Mouse
    • Rat
    • Cow
    • Dog
    • Guinea Pig
    • Zebrafish (Danio rerio)
    • Hamster
    • Horse
    • Monkey
    • Pig
    • Rabbit
  • 论文引用
  • 图像
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 25G46
    • 2G7
    • 3C6
    • 500000500000
    • 5E5
    • 5H49
    • RB18979
  • 抗原表位
    • AA 541-640
    • AA 601-952
    • AA 1-952
    • AA 761-919
    • N-Term
    • AA 174-203
    • AA 595-770
    • AA 70-225
    • AA 70-245
    • AA 755-953
    • AA 782-953
    • Middle Region
    • AA 173-203
    • AA 218-267
    • AA 350-450
    • AA 494-527
    • AA 851-952
    • C-Term
  • 标记
    • 非结合性
    • FITC
    • Biotin
    • HRP
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
  • 抗体亚型
    • IgG
    • Ig Fraction
    • IgG1
    • IgG2b
  • 蛋白类型
    • Recombinant Antibody
  • Format
    • Liquid
    • Lyophilized
  • Grade
    • KO Validated
  • Supplier
    • antibodies-online
    • Biomatik
    • Abbexa
    • Boster Bio
    • Cloud-Clone
    • USBio
    • Abcepta
    • Aviva Systems Biology
    • RayBiotech

Latest Publications for our GAA 抗体

Xiao, Westbroek, Motabar, Lea, Hu, Velayati, Zheng, Southall, Gustafson, Goldin, Sidransky, Liu, Simeonov, Tamargo, Ribes, Matalonga, Ferrer, Marugan: "Discovery of a novel noniminosugar acid ? glucosidase chaperone series." in: Journal of medicinal chemistry, Vol. 55, Issue 17, pp. 7546-59, (2012) (PubMed).

Cheray, Petit, Forestier, Karayan-Tapon, Maftah, Jauberteau, Battu, Gallet, Lalloué: "Glycosylation-related gene expression is linked to differentiation status in glioblastomas undifferentiated cells." in: Cancer letters, Vol. 312, Issue 1, pp. 24-32, (2011) (PubMed).

Aliases for GAA 抗体

glucosidase alpha, acid (GAA) 抗体
glucosidase, alpha, acid (Gaa) 抗体
transmembrane and coiled-coil domain family 1 (TMCC1) 抗体
glucosidase, alpha; acid (Pompe disease, glycogen storage disease type II) (gaa) 抗体
glucosidase alpha, acid (Gaa) 抗体
E430018M07Rik 抗体
LYAG 抗体
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