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DARS2 抗体

(Aspartyl-tRNA Synthetase 2, Mitochondrial (DARS2))
The protein encoded by this gene belongs to the class-II aminoacyl-tRNA synthetase family. It is a mitochondrial enzyme that specifically aminoacylates aspartyl-tRNA. Mutations in this gene are associated with leukoencephalopathy with brainstem and spinal cord involvement and lactate elevation (LBSL). [provided by RefSeq, Nov 2009].

35 results

DARS2 适用: 人, 大鼠 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 350
产品编号 ABIN2809095
 
DARS2 适用: 人 ELISA 宿主: 兔 Polyclonal HRP
产品编号 ABIN7144752
 
DARS2 适用: 人 ELISA 宿主: 兔 Polyclonal Biotin
产品编号 ABIN7144750
 
DARS2 适用: 人 宿主: 兔 Polyclonal FITC
产品编号 ABIN7144751
 
DARS2 适用: 人, 小鼠, 大鼠 WB, ICC, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7093856
 
DARS2 适用: 人, 小鼠 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7111762
 
DARS2 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7568181
 
DARS2 适用: 人 WB, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7466617
 
DARS2 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN2597854
 
DARS2 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2597855
 
DARS2 适用: 人 WB, IHC, ELISA, ICC, IF, FACS 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6719279
 
DARS2 适用: 小鼠 WB, IHC, ICC, IP 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7612360
 
DARS2 适用: 人 ELISA 宿主: 兔 Polyclonal FITC
产品编号 ABIN6081269
 
DARS2 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1083186
 
DARS2 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7615851
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • ELISA
    • Immunohistochemistry (IHC)
    • Immunocytochemistry (ICC)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Immunofluorescence (IF)
    • Immunoprecipitation (IP)
    • Flow Cytometry (FACS)
  • 适用
    • Human
    • Rat
    • Mouse
  • 图像
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
  • 克隆形成能力
    • Polyclonal
  • 抗原表位
    • AA 551-645
    • AA 489-628
    • AA 1-645
    • AA 390-653
    • AA 334-448
    • AA 406-645
    • AA 59-645
    • Internal Region
    • Mitochondrial
  • 标记
    • 非结合性
    • FITC
    • Biotin
    • HRP
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
  • 抗体亚型
    • IgG
  • Format
    • Liquid
    • Lyophilized
  • Supplier
    • antibodies-online
    • Biomatik
    • Abbexa
    • Boster Bio
    • CUSABIO

Latest Publications for our DARS2 抗体

Scheper, van der Klok, van Andel, van Berkel, Sissler, Smet, Muravina, Serkov, Uziel, Bugiani, Schiffmann, Krägeloh-Mann, Smeitink, Florentz, Van Coster, Pronk, van der Knaap: "Mitochondrial aspartyl-tRNA synthetase deficiency causes leukoencephalopathy with brain stem and spinal cord involvement and lactate elevation." in: Nature genetics, Vol. 39, Issue 4, pp. 534-9, (2007) (PubMed).

Bonnefond, Fender, Rudinger-Thirion, Giegé, Florentz, Sissler: "Toward the full set of human mitochondrial aminoacyl-tRNA synthetases: characterization of AspRS and TyrRS." in: Biochemistry, Vol. 44, Issue 12, pp. 4805-16, (2005) (PubMed).

Aliases for DARS2 抗体

aspartyl-tRNA synthetase 2, mitochondrial (DARS2) 抗体
aspartyl-tRNA synthetase 2, mitochondrial (dars2) 抗体
aspartate--tRNA ligase, mitochondrial (LOC100547893) 抗体
aspartyl-tRNA synthetase 2 (mitochondrial) (Dars2) 抗体
5830468K18Rik 抗体
ASPRS 抗体
LBSL 抗体
MT-ASPRS 抗体
RGD1308286 抗体
RP3-383J4.2 抗体
si:dkey-21n10.1 抗体
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