CTNS 产品
(Cystinosis, Nephropathic (CTNS))
Categories
This gene encodes a seven-transmembrane domain protein that functions to transport cystine out of lysosomes. Its activity is driven by the H+ electrochemical gradient of the lysosomal membrane. Mutations in this gene cause cystinosis, a lysosomal storage disorder. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jul 2009].
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Featured CTNS Categories
CTNS 抗体
High quality antibodies with extensive validation data.
CTNS ELISA试剂盒
Reliable ELISA kits for a wide range of species.
CTNS 蛋白
Proteins for various applications incl. WB, ELISA, IF etc.
Recommended CTNS 抗体
Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity
Human
Application
WB, ELISA
Validations
- (2)
- (6)
Cat. No.
ABIN560527
Quantity
100 μg
Datasheet
Datasheet
Reactivity
Human
Application
WB
Validations
- (1)
- (2)
Cat. No.
ABIN514757
Quantity
100 μg
Datasheet
Datasheet
Reactivity
Human
Application
WB
Validations
- (5)
- (1)
Cat. No.
ABIN1881240
Quantity
400 μL
Datasheet
Datasheet
Recommended CTNS ELISA试剂盒
Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity
Human
Analytical Method
Validations
Cat. No.
ABIN1128563
Quantity
96 tests
Datasheet
Datasheet
Reactivity
Mouse
Analytical Method
Validations
Cat. No.
ABIN1128564
Quantity
96 tests
Datasheet
Datasheet
Reactivity
Cow
Analytical Method
Validations
Cat. No.
ABIN1128562
Quantity
96 tests
Datasheet
Datasheet
Recommended CTNS 蛋白
Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity
Human
Source
Wheat germ
Validations
- (1)
Cat. No.
ABIN1350684
Quantity
10 μg
Datasheet
Datasheet
Reactivity
Human
Source
Wheat germ
Validations
- (1)
Cat. No.
ABIN1777330
Quantity
10 μg
Datasheet
Datasheet
Reactivity
Human
Source
Tobacco (Nicotiana tabacum)
Validations
- (1)
Cat. No.
ABIN3110520
Quantity
1 mg
Datasheet
Datasheet
Latest Publications for our CTNS Products
: "Cystine accumulation attenuates insulin release from the pancreatic β-cell due to elevated oxidative stress and decreased ATP levels." in: The Journal of physiology, Vol. 593, Issue 23, pp. 5167-82, (2015) (PubMed).: "Cystine dimethylester loading promotes oxidative stress and a reduction in ATP independent of lysosomal cystine accumulation in a human proximal tubular epithelial cell line." in: Experimental physiology, Vol. 98, Issue 10, pp. 1505-17, (2013) (PubMed).
: "Modulation of CTNS gene expression by intracellular thiols." in: Free radical biology & medicine, Vol. 48, Issue 7, pp. 865-72, (2010) (PubMed).
: "Analysis of CTNS gene transcripts in nephropathic cystinosis." in: Pediatric nephrology (Berlin, Germany), Vol. 25, Issue 7, pp. 1263-7, (2010) (PubMed).
: "A futile cycle, formed between two ATP-dependant gamma-glutamyl cycle enzymes, gamma-glutamyl cysteine synthetase and 5-oxoprolinase: the cause of cellular ATP depletion in nephrotic cystinosis?" in: Journal of biosciences, Vol. 35, Issue 1, pp. 21-5, (2010) (PubMed).
: "Characterization of CTNS mutations in Arab patients with cystinosis." in: Ophthalmic genetics, Vol. 30, Issue 4, pp. 185-9, (2009) (PubMed).
: "Analysis of the CTNS gene in 32 cystinosis patients from Spain." in: Clinical genetics, Vol. 76, Issue 5, pp. 486-9, (2009) (PubMed).
Synonyms and alternative names related to CTNS
cystinosin, lysosomal cystine transporter (CTNS), cystinosin, lysosomal cystine transporter (Ctns), cystinosis, nephropathic (Ctns), cystinosin, lysosomal cystine transporter (ctns), cystinosis, nephropathic (CTNS), cystinosin, lysosomal cystine transporter L homeolog (ctns.L), AI195360, AW049661, CTNS, CTNS-LSB, PQLC4, zgc:110194Protein level used designations for CTNS
- cystinosin
- cystinosis, nephropathic
- cystinosin-like
- cystinosin, lysosomal cystine transporter
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