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BTD 产品

(Biotinidase (BTD))

Categories

Biotinidase functions to recycle biotin in the body by cleaving biocytin (biotin-epsilon-lysine), a normal product of carboxylase degradation, resulting in regeneration of free biotin. Biotinidase has also been shown to have biotinyl-transferase activity. Defects in the biotinidase gene cause multiple carboxylase deficiency. [provided by RefSeq, Jul 2008].

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Featured BTD Categories

BTD 抗体

High quality antibodies with extensive validation data.

BTD ELISA试剂盒

Reliable ELISA kits for a wide range of species.

BTD 蛋白

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended BTD 抗体

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, IHC
Validations
  • (4)
Cat. No. ABIN6137680
Quantity 100 μL
Datasheet Datasheet
Reactivity Human, Mouse, Rat
Application IHC
Validations
  • (3)
Cat. No. ABIN7262090
Quantity 200 μL
Datasheet Datasheet
Reactivity Human
Application WB, ELISA, IP
Validations
  • (3)
Cat. No. ABIN560100
Quantity 100 μg
Datasheet Datasheet

Recommended BTD ELISA试剂盒

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Competition ELISA
Validations
  • (1)
Cat. No. ABIN6975618
Quantity 96 tests
Datasheet Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
Cat. No. ABIN6954108
Quantity 96 tests
Datasheet Datasheet
Reactivity Mouse
Analytical Method
Validations
Cat. No. ABIN1123912
Quantity 96 tests
Datasheet Datasheet

Recommended BTD 蛋白

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1346941
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Insect Cells
Validations
  • (1)
Cat. No. ABIN3090517
Quantity 1 mg
Datasheet Datasheet
Reactivity Mouse
Source Insect Cells
Validations
  • (1)
Cat. No. ABIN3126087
Quantity 1 mg
Datasheet Datasheet

Latest Publications for our BTD Products

Cowan, Blitzer, Wolf: "Technical standards and guidelines for the diagnosis of biotinidase deficiency." in: Genetics in medicine : official journal of the American College of Medical Genetics, Vol. 12, Issue 7, pp. 464-70, (2010) (PubMed).

Synonyms and alternative names related to BTD

Biotinidase (Btnd), biotinidase (btd), biotinidase (BTD), biotinidase (Btd), Biotinase, BTD, CG3599, CT12113, Dmel\\CG3599, zgc:153333

Protein level used designations for BTD

  • biotinidase
  • CG3599-PA
  • Btd-PA
  • biotinidase-like
  • biotinase
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