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Ataxin 3 抗体

(Ataxin 3 (ATXN3))
Machado-Joseph disease, also known as spinocerebellar ataxia-3, is an autosomal dominant neurologic disorder. The protein encoded by this gene contains (CAG)n repeats in the coding region, and the expansion of these repeats from the normal 13-36 to 68-79 is one cause of Machado-Joseph disease. There is a negative correlation between the age of onset and CAG repeat numbers. Alternatively spliced transcript variants encoding different isoforms have been described for this gene. [provided by RefSeq, Sep 2009].

58 results

ATXN3 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal FITC
产品编号 ABIN6986897
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy5.5
产品编号 ABIN6985175
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy7
产品编号 ABIN6986036
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC (p), IHC (fro) 宿主: 兔 Polyclonal HRP
产品编号 ABIN6987557
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy3
产品编号 ABIN6983453
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal Cy5
产品编号 ABIN6984314
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 555
产品编号 ABIN6978377
 
ATXN3 适用: 人 ELISA 宿主: 兔 Polyclonal HRP
产品编号 ABIN7144796
 
ATXN3 适用: 人 宿主: 兔 Polyclonal FITC
产品编号 ABIN7144795
 
ATXN3 适用: 人 ELISA 宿主: 兔 Polyclonal Biotin
产品编号 ABIN7144794
 
ATXN3 适用: 人, 小鼠, 大鼠 WB, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6388309
 
ATXN3 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7568185
 
ATXN3 适用: 人 WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1841430
 
ATXN3 适用: 人, 小鼠, 大鼠, Cow, 绵羊, 马, 兔, 豚鼠, 犬, 猴, Pig, Cat, 小鸡, 驴, 山羊, Hamster WB 宿主: 山羊 Polyclonal unconjugated
产品编号 ABIN2617361
 
ATXN3 适用: 人, 小鼠 WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1833855
 
ATXN3 适用: 人 WB, ELISA, IHC, FACS 宿主: 兔 Polyclonal FITC
产品编号 ABIN1969843
 
ATXN3 适用: 人 WB, ELISA, IHC, FACS 宿主: 兔 Polyclonal HRP
产品编号 ABIN1972104
 
ATXN3 适用: 人 WB, ELISA, IHC, FACS 宿主: 兔 Polyclonal PE
产品编号 ABIN1974432
 
ATXN3 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2589471
 
ATXN3 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal APC
产品编号 ABIN1963396
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • ELISA
    • Immunohistochemistry (IHC)
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Flow Cytometry (FACS)
    • Immunofluorescence (IF)
    • Immunocytochemistry (ICC)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Immunoprecipitation (IP)
    • Enzyme Immunoassay (EIA)
    • Immunochromatography (IC)
    • Immunohistochemistry (Formalin-fixed Paraffin-embedded Sections) (IHC (fp))
  • 适用
    • Human
    • Mouse
    • Rat
    • Cow
    • Horse
    • Sheep
    • Dog
    • Guinea Pig
    • Monkey
    • Pig
    • Rabbit
    • Cat
    • Chicken
    • Donkey
    • Goat
    • Hamster
    • Avian
    • Zebrafish (Danio rerio)
  • 论文引用
  • 图像
  • 仅无防腐剂
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Goat
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 2SCA-1H9
    • RB23951
    • RB4606
  • 抗原表位
    • AA 51-150
    • AA 29-59
    • AA 1-288
    • pSer256
    • AA 267-297
    • N-Term
    • AA 1-245
    • AA 120-250
    • C-Term
    • AA 1-182
    • AA 1-215
    • AA 1-364
    • AA 200-280
    • AA 226-254
    • AA 261-288
    • AA 35-84
    • Middle Region
  • 标记
    • 非结合性
    • FITC
    • HRP
    • Biotin
    • PE
    • APC
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
  • 抗体亚型
    • IgG
    • Ig Fraction
    • IgG1 kappa
  • Format
    • Liquid
    • Lyophilized
  • Grade
    • KO Validated
  • Supplier
    • antibodies-online
    • Signalway
    • Abbexa
    • Abcepta
    • Acris
    • Aviva Systems Biology
    • Biomatik
    • Boster Bio
    • Cohesion Biosciences
    • ProteoGenix
    • RayBiotech
    • USBio

Latest Publications for our Ataxin 3 抗体

Hsu, Jhang, Cheng, Chang, Mao, Yang, Lin, Chen, Yang: "The Truncated C-terminal Fragment of Mutant ATXN3 Disrupts Mitochondria Dynamics in Spinocerebellar Ataxia Type 3 Models." in: Frontiers in molecular neuroscience, Vol. 10, pp. 196, (2017) (PubMed).

Zeng, Tang, Ma: "Ataxin-3 expression correlates with the clinicopathologic features of gastric cancer." in: International journal of clinical and experimental medicine, Vol. 7, Issue 4, pp. 973-81, (2014) (PubMed).

Michlewski, Krzyzosiak: "Molecular architecture of CAG repeats in human disease related transcripts." in: Journal of molecular biology, Vol. 340, Issue 4, pp. 665-79, (2004) (PubMed).

Li, Yokota, Matsumura, Taira, Mizusawa: "Sequence-dependent and independent inhibition specific for mutant ataxin-3 by small interfering RNA." in: Annals of neurology, Vol. 56, Issue 1, pp. 124-9, (2004) (PubMed).

Albrecht, Golatta, Wüllner, Lengauer: "Structural and functional analysis of ataxin-2 and ataxin-3." in: European journal of biochemistry / FEBS, Vol. 271, Issue 15, pp. 3155-70, (2004) (PubMed).

Aspberg, Miura, Bourdoulous, Shimonaka, Heinegârd, Schachner, Ruoslahti, Yamaguchi: "The C-type lectin domains of lecticans, a family of aggregating chondroitin sulfate proteoglycans, bind tenascin-R by protein-protein interactions independent of carbohydrate moiety." in: Proceedings of the National Academy of Sciences of the United States of America, Vol. 94, Issue 19, pp. 10116-21, (1997) (PubMed).

Paulson, Das, Crino, Perez, Patel, Gotsdiner, Fischbeck, Pittman: "Machado-Joseph disease gene product is a cytoplasmic protein widely expressed in brain." in: Annals of neurology, Vol. 41, Issue 4, pp. 453-62, (1997) (PubMed).

Aliases for Ataxin 3 抗体

ataxin 3 (atxn3) 抗体
ataxin 3 (ATXN3) 抗体
ataxin 3 L homeolog (atxn3.L) 抗体
ataxin-3 (MICPUN_104046) 抗体
ataxin-3 (MICPUCDRAFT_46658) 抗体
ataxin 3 (Atxn3) 抗体
2210008M02Rik 抗体
AI463012 抗体
AI647473 抗体
at3 抗体
AT3 抗体
ataxin-3 抗体
atx3 抗体
ATX3 抗体
ATXN3 抗体
jos 抗体
JOS 抗体
MGC83584 抗体
Mjd 抗体
mjd 抗体
MJD 抗体
mjd1 抗体
MJD1 抗体
Rsca3 抗体
sca3 抗体
SCA3 抗体
Sca3 抗体
zgc:56323 抗体
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