MCCC2 抗体 (AA 21-330)
Quick Overview for MCCC2 抗体 (AA 21-330) (ABIN7600614)
抗原
See all MCCC2 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 21-330
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原理
- Anti-MCCC2 Antibody Picoband®
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交叉反应 （详细）
- No cross-reactivity with other proteins.
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产品特性
- Anti-MCCC2 Antibody Picoband® (ABIN7600614). Tested in ELISA, IHC, WB, Flow Cytometry applications. This antibody reacts with Human, Mouse, Rat. The brand Picoband indicates this is a premium antibody that guarantees superior quality, high affinity, and strong signals with minimal background in Western blot applications. Only our best-performing antibodies are designated as Picoband, ensuring unmatched performance.
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纯化方法
- Immunogen affinity purified.
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免疫原
- E.coli-derived human MCCC2 recombinant protein (Position: R21-D330).
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亚型
- IgG
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anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) (AA 1-563) antibody
MCCC2 适用: 人 WB, IF 宿主: 小鼠 Polyclonal unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) (AA 1-563) antibodyMCCC2 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) (AA 456-563) antibodyMCCC2 适用: 人 WB, ELISA, IHC (p) 宿主: 小鼠 Monoclonal 2B3 unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) (Center) antibodyMCCC2 适用: 人, 小鼠 WB, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) (AA 284-563) antibodyMCCC2 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) (AA 456-563) antibodyMCCC2 适用: 人 WB, ELISA 宿主: 小鼠 Polyclonal unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) (AA 284-563) antibodyMCCC2 适用: 人 WB, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) (AA 163-189) antibodyMCCC2 适用: 人, 大鼠 WB, IHC (p), FACS 宿主: 兔 Polyclonal RB21307 unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) antibodyMCCC2 适用: 人, 大鼠 WB, IHC, FACS 宿主: 兔 Polyclonal unconjugated
anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) (AA 380-563) antibodyMCCC2 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
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应用备注
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Western blot, 0.1-0.25 μg/mL, Human, Mouse, Rat
Immunohistochemistry, 2-5 μg/mL, Human, Mouse, Rat
Flow Cytometry (Fixed), 1-3 μg/1x106 cells, Human
ELISA, 0.1-0.5 μg/mL, -
1. Bannwart, C., Wermuth, B., Baumgartner, R., Suormala, T., Wiesmann, U. N. Isolated biotin-resistant deficiency of 3-methylcrotonyl-CoA carboxylase presenting as a clinically severe form in a newborn with fatal outcome. J. Inherit. Metab. Dis. 15: 863-868, 1992. 2. Baumgartner, M. R., Almashanu, S., Suormala, T., Obie, C., Cole, R. N., Packman, S., Baumgartner, E. R., Valle, D. The molecular basis of human 3-methylcrotonyl-CoA carboxylase deficiency. J. Clin. Invest. 107: 495-504, 2001. 3. Baykal, T., Gokcay, G. H., Ince, Z., Dantas, M. F., Fowler, B., Baumgartner, M. R., Demir, F., Can, G., Demirkol, M. Consanguineous 3-methylcrotonyl-CoA carboxylase deficiency: early-onset necrotizing encephalopathy with lethal outcome. J. Inherit. Metab. Dis. 28: 229-233, 2005. -
限制
- 仅限研究用
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状态
- Lyophilized
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溶解方式
- Adding 0.2 mL of distilled water will yield a concentration of 500 μg/mL.
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浓度
- 500 μg/mL
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缓冲液
- Each vial contains 4 mg Trehalose, 0.9 mg NaCl, 0.2 mg Na2HPO4.
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储存条件
- 4 °C,-20 °C
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储存方法
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At -20°C for one year from date of receipt. After reconstitution, at 4°C for one month.
It can also be aliquotted and stored frozen at -20°C for six months. Avoid repeated freezing and thawing.
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- MCCC2 (Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
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别名
- MCCC2
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背景
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Synonyms: Homeobox protein SIX6,Homeodomain protein OPTX2,Optic homeobox 2,Sine oculis homeobox homolog 6,SIX6,OPTX2, SIX9,
Tissue Specificity: Expressed in the developing and adult retina. Also expressed in the hypothalamic and the pituitary regions.
Background: This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. Alternative splicing results in multiple transcript variants encoding distinct isoforms.
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分子量
- 61 kDa
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基因ID
- 64087
抗原
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