GCH1 抗体
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北京 101111
Quick Overview for GCH1 抗体 (ABIN7190766)
抗原
See all GCH1 抗体适用
宿主
克隆类型
标记
应用范围
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原理
- GCH1 Antibody
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纯化方法
- Antigen affinity purification
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免疫原
- Synthetic peptide of Human GCH1
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亚型
- IgG
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anti-GTP Cyclohydrolase 1 (GCH1) (AA 84-172) antibody
GCH1 适用: 人 WB, ELISA, IHC (p), IP 宿主: 小鼠 Monoclonal 4A12 unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (Internal Region) antibodyVerified GCH1 适用: 人 ELISA, IHC 宿主: 山羊 Polyclonal unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) antibodyKD Validated GCH1 适用: 人 WB 宿主: 小鼠 Monoclonal 24GB13125 unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (AA 1-250) antibodyGCH1 适用: 人 WB, IF 宿主: 小鼠 Polyclonal unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (AA 1-250) antibodyGCH1 适用: 人 ELISA, IF 宿主: 小鼠 Monoclonal 2C4 unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (AA 1-250) antibodyGCH1 适用: 人 ELISA, IF 宿主: 小鼠 Monoclonal 1F5 unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (AA 34-110) antibodyGCH1 适用: 小鼠 WB, ELISA, IF (cc), IF (p), IHC (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (AA 84-172) antibodyGCH1 适用: 人 WB, ELISA 宿主: 小鼠 Polyclonal unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (AA 1-250) antibodyGCH1 适用: 人 WB, ELISA 宿主: 小鼠 Polyclonal unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (C-Term) antibodyGCH1 适用: 人, 小鼠, 大鼠, Cow, 犬, 兔, 豚鼠, 马, Pig, Bat, 小鸡, Hamster, 猴, 非洲爪蟾 WB 宿主: 兔 Polyclonal unconjugated
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应用备注
- Optimal working dilution should be determined by the investigator.
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- pH 7.4 PBS, 0.05 % Sodium azide, 40 % Glycerol
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C,-80 °C
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储存方法
- Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
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- GCH1 (GTP Cyclohydrolase 1 (GCH1))
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别名
- GCH1
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背景
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Background: This gene encodes a member of the GTP cyclohydrolase family. The encoded protein is the first and rate-limiting enzyme in tetrahydrobiopterin (BH4) biosynthesis, catalyzing the conversion of GTP into 7,8-dihydroneopterin triphosphate. BH4 is an essential cofactor required by aromatic amino acid hydroxylases as well as nitric oxide synthases. Mutations in this gene are associated with malignant hyperphenylalaninemia and dopa-responsive dystonia. Several alternatively spliced transcript variants encoding different isoforms have been described, however, not all variants give rise to a functional enzyme.
Aliases: dystonia 14 antibody, DYT 5 antibody, DYT14 antibody, DYT5 antibody, DYT5a antibody, GCH 1 antibody, GCH antibody, Gch1 antibody, GCH1_HUMAN antibody, GTP CH 1 antibody, GTP CH I antibody, GTP cyclohydrolase 1 (dopa responsive dystonia) antibody, GTP cyclohydrolase 1 antibody, GTP cyclohydrolase I antibody, GTP-CH-I antibody, GTPCH 1 antibody, GTPCH1 antibody, Guanosine 5' triphosphate cyclohydrolase I antibody, HPABH4B antibody
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UniProt
- P30793
抗原
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