GAA 抗体 (N-Term)
Quick Overview for GAA 抗体 (N-Term) (ABIN635720)
抗原
See all GAA 抗体适用
宿主
克隆类型
标记
应用范围
-
-
抗原表位
- N-Term
-
特异性
- GAA antibody was raised against the N terminal of GAA
-
纯化方法
- Affinity purified
-
免疫原
- GAA antibody was raised using the N terminal of GAA corresponding to a region with amino acids FGVIVRRQLDGRVLLNTTVAPLFFADQFLQLSTSLPSQYITGLAEHLSPL
-
-
-
-
应用备注
-
WB: 1 µg/mL
Optimal conditions should be determined by the investigator. -
说明
-
GAA Blocking Peptide, (ABIN938303), is also available for use as a blocking control in assays to test for specificity of this GAA antibody
-
限制
- 仅限研究用
-
-
-
状态
- Lyophilized
-
溶解方式
- Lyophilized powder. Add distilled water for a 1 mg/mL concentration of GAA antibody in PBS
-
浓度
- Lot specific
-
缓冲液
- PBS
-
注意事项
-
Avoid repeated freeze/thaw cycles.
Dilute only prior to immediate use. -
储存条件
- 4 °C/-20 °C
-
储存方法
- Store at 2-8 °C for short periods. For longer periods of storage, store at -20 °C.
-
-
- GAA (Glucosidase, Alpha, Acid (GAA))
-
别名
- GAA
-
背景
- GAA is acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum.
-
分子量
- 98 kDa (MW of target protein)
-
途径
- Cellular Glucan Metabolic Process
抗原
-