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GAA 抗体 (N-Term)

This anti-GAA antibody is a 兔 多克隆 antibody detecting GAA in WB. Suitable for 人.
产品编号 ABIN635720
发货至: 中国

Quick Overview for GAA 抗体 (N-Term) (ABIN635720)

抗原

See all GAA 抗体
GAA (Glucosidase, Alpha, Acid (GAA))

适用

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宿主

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克隆类型

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多克隆

标记

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This GAA antibody is un-conjugated

应用范围

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Western Blotting (WB)
  • 抗原表位

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    N-Term

    特异性

    GAA antibody was raised against the N terminal of GAA

    纯化方法

    Affinity purified

    免疫原

    GAA antibody was raised using the N terminal of GAA corresponding to a region with amino acids FGVIVRRQLDGRVLLNTTVAPLFFADQFLQLSTSLPSQYITGLAEHLSPL
  • 应用备注

    WB: 1 µg/mL
    Optimal conditions should be determined by the investigator.

    说明

    GAA Blocking Peptide, (ABIN938303), is also available for use as a blocking control in assays to test for specificity of this GAA antibody

    限制

    仅限研究用
  • 状态

    Lyophilized

    溶解方式

    Lyophilized powder. Add distilled water for a 1 mg/mL concentration of GAA antibody in PBS

    浓度

    Lot specific

    缓冲液

    PBS

    注意事项

    Avoid repeated freeze/thaw cycles.
    Dilute only prior to immediate use.

    储存条件

    4 °C/-20 °C

    储存方法

    Store at 2-8 °C for short periods. For longer periods of storage, store at -20 °C.
  • 抗原

    GAA (Glucosidase, Alpha, Acid (GAA))

    别名

    GAA

    背景

    GAA is acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum.

    分子量

    98 kDa (MW of target protein)

    途径

    Cellular Glucan Metabolic Process
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