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ABCD1 产品

(ATP-Binding Cassette, Sub-Family D (Ald), Member 1 (ABCD1))

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The protein encoded by this gene is a member of the superfamily of ATP-binding cassette (ABC) transporters. ABC proteins transport various molecules across extra- and intra-cellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the ALD subfamily, which is involved in peroxisomal import of fatty acids and/or fatty acyl-CoAs in the organelle. All known peroxisomal ABC transporters are half transporters which require a partner half transporter molecule to form a functional homodimeric or heterodimeric transporter. This peroxisomal membrane protein is likely involved in the peroxisomal transport or catabolism of very long chain fatty acids. Defects in this gene have been identified as the underlying cause of adrenoleukodystrophy, an X-chromosome recessively inherited demyelinating disorder of the nervous system. [provided by RefSeq, Jul 2008].

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Featured ABCD1 Categories

ABCD1 抗体

High quality antibodies with extensive validation data.

ABCD1 ELISA试剂盒

Reliable ELISA kits for a wide range of species.

ABCD1 蛋白

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended ABCD1 抗体

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, FACS, IHC (p)
Validations
  • (4)
Cat. No. ABIN654412
Quantity 400 μL
Datasheet Datasheet
Reactivity Human, Mouse
Application ELISA, IHC
Validations
  • (2)
Cat. No. ABIN7248188
Quantity 200 μL
Datasheet Datasheet
Reactivity Human
Application WB, ELISA, IF, ICC
Validations
  • (2)
Cat. No. ABIN6257662
Quantity 100 μL
Datasheet Datasheet

Recommended ABCD1 ELISA试剂盒

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
Cat. No. ABIN6953987
Quantity 96 tests
Datasheet Datasheet
Reactivity Various Species
Analytical Method Quantitative Competition ELISA
Validations
Cat. No. ABIN5593403
Quantity 96 tests
Datasheet Datasheet
Reactivity Rat
Analytical Method Quantitative Competition ELISA
Validations
Cat. No. ABIN956343
Quantity 96 tests
Datasheet Datasheet

Recommended ABCD1 蛋白

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Escherichia coli (E. coli)
Validations
  • (1)
Cat. No. ABIN7121932
Quantity 50 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1305469
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1305471
Quantity 10 μg
Datasheet Datasheet

Latest Publications for our ABCD1 Products

Gong, Sasidharan, Laheji, Frosch, Musolino, Tanzi, Kim, Biffi, El Khoury, Eichler: "Microglial dysfunction as a key pathological change in adrenomyeloneuropathy." in: Annals of neurology, Vol. 82, Issue 5, pp. 813-827, (2017) (PubMed).

Musolino, Gong, Snyder, Jimenez, Lok, Lo, Moser, Grabowski, Frosch, Eichler: "Brain endothelial dysfunction in cerebral adrenoleukodystrophy." in: Brain : a journal of neurology, Vol. 138, Issue Pt 11, pp. 3206-20, (2015) (PubMed).

Vera-Estrella, Barkla, Pantoja: "Comparative 2D-DIGE analysis of salinity responsive microsomal proteins from leaves of salt-sensitive Arabidopsis thaliana and salt-tolerant Thellungiella salsuginea." in: Journal of proteomics, Vol. 111, pp. 113-27, (2014) (PubMed).

Sun, Suen, Zhang, Liang, Carrie, Whelan, Ward, Hawkins, Jiang, Lim: "A dual-targeted purple acid phosphatase in Arabidopsis thaliana moderates carbon metabolism and its overexpression leads to faster plant growth and higher seed yield." in: The New phytologist, Vol. 194, Issue 1, pp. 206-19, (2012) (PubMed).

Höftberger, Kunze, Weinhofer, Aboul-Enein, Voigtländer, Oezen, Amann, Bernheimer, Budka, Berger: "Distribution and cellular localization of adrenoleukodystrophy protein in human tissues: implications for X-linked adrenoleukodystrophy." in: Neurobiology of disease, Vol. 28, Issue 2, pp. 165-74, (2007) (PubMed).

Synonyms and alternative names related to ABCD1

ATP binding cassette subfamily D member 1 (ABCD1), ATP binding cassette subfamily D member 1 (Abcd1), ATP-binding cassette, sub-family D (ALD), member 1 (abcd1), ATP-binding cassette sub-family D member 1 (CpipJ_CPIJ013253), ATP-binding cassette sub-family D member 1 (VDBG_05717), ATP-binding cassette, sub-family D (ALD), member 1 (Abcd1), ATP binding cassette subfamily D member 1 L homeolog (abcd1.L), ATP binding cassette subfamily D member 1 (abcd1), ABC42, ABCD1, ALD, Ald, Aldgh, ALDP, AMN, RGD1562128, zgc:172102

Protein level used designations for ABCD1

  • ATP-binding cassette sub-family D member 1
  • adrenoleukodystrophy protein
  • ATP-binding cassette, sub-family D (ALD), member 1
  • ATP-binding cassette, sub-family D, member 1
  • X-linked adrenoleukodystrophy (ALD) gene homolog
  • ATP-binding cassette sub-family D member 1-like
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