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SUCLA2 产品

(Succinate-CoA Ligase, ADP-Forming, beta Subunit (SUCLA2))

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Succinyl-CoA synthetase (SCS) is a mitochondrial matrix enzyme that acts as a heterodimer, being composed of an invariant alpha subunit and a substrate-specific beta subunit. The protein encoded by this gene is an ATP-specific SCS beta subunit that dimerizes with the SCS alpha subunit to form SCS-A, an essential component of the tricarboxylic acid cycle. SCS-A hydrolyzes ATP to convert succinate to succinyl-CoA. Defects in this gene are a cause of myopathic mitochondrial DNA depletion syndrome. A pseudogene of this gene has been found on chromosome 6. [provided by RefSeq, Jul 2008].

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Featured SUCLA2 Categories

SUCLA2 抗体

High quality antibodies with extensive validation data.

SUCLA2 蛋白

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended SUCLA2 抗体

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, ICC, IF, IHC (p)
Validations
  • (5)
Cat. No. ABIN2856701
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, IHC, ELISA
Validations
  • (3)
Cat. No. ABIN7170910
Quantity 100 μL
Datasheet Datasheet
Reactivity Human, Mouse, Rat
Application WB, IHC, ICC, IF
Validations
  • (3)
Cat. No. ABIN6265362
Quantity 100 μL
Datasheet Datasheet

Recommended SUCLA2 ELISA试剂盒

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
Cat. No. ABIN6233603
Quantity 96 tests
Datasheet Datasheet

Recommended SUCLA2 蛋白

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1321839
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Insect Cells
Validations
  • (1)
Cat. No. ABIN3077520
Quantity 1 mg
Datasheet Datasheet
Reactivity Mouse
Source Insect Cells
Validations
  • (1)
Cat. No. ABIN3120394
Quantity 1 mg
Datasheet Datasheet

Latest Publications for our SUCLA2 Products

Bishop, Tchaikovskii, Hoffbrand, Fraser, Margolis: "X-linked sideroblastic anemia due to carboxyl-terminal ALAS2 mutations that cause loss of binding to the β-subunit of succinyl-CoA synthetase (SUCLA2)." in: The Journal of biological chemistry, Vol. 287, Issue 34, pp. 28943-55, (2012) (PubMed).

Synonyms and alternative names related to SUCLA2

succinate-Coenzyme A ligase, ADP-forming, beta subunit (Sucla2), succinate-CoA ligase ADP-forming beta subunit (SUCLA2), 4930547K18Rik, A-BETA, MTDPS5, SCS, SCS-betaA

Protein level used designations for SUCLA2

  • ATP-specific succinyl-CoA synthetase subunit beta
  • SCS-betaA
  • succinyl-CoA ligase [ADP-forming] subunit beta, mitochondrial
  • succinyl-CoA synthetase beta-A chain
  • ATP-specific succinyl-CoA synthetase, beta subunit
  • mitochondrial succinyl-CoA ligase [ADP-forming] subunit beta
  • renal carcinoma antigen NY-REN-39
  • ATP-specific succinyl-CoA synthetase beta
  • Succinyl-CoA ligase [ADP-forming] beta-chain, mitochondrial
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