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SGSH 产品

(N-Sulfoglucosamine Sulfohydrolase (SGSH))

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This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jul 2008].

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Featured SGSH Categories

SGSH 抗体

High quality antibodies with extensive validation data.

SGSH ELISA试剂盒

Reliable ELISA kits for a wide range of species.

SGSH 蛋白

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended SGSH 抗体

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, IHC, IP, ICC
Validations
  • (5)
Cat. No. ABIN7436429
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, IP
Validations
  • (3)
Cat. No. ABIN948461
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application IHC, ELISA
Validations
  • (2)
Cat. No. ABIN7160782
Quantity 100 μL
Datasheet Datasheet

Recommended SGSH ELISA试剂盒

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
Cat. No. ABIN6975572
Quantity 96 tests
Datasheet Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
Cat. No. ABIN6958016
Quantity 96 tests
Datasheet Datasheet
Reactivity Mouse
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
Cat. No. ABIN6958017
Quantity 96 tests
Datasheet Datasheet

Recommended SGSH 蛋白

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1319846
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Insect Cells
Validations
  • (1)
Cat. No. ABIN3077378
Quantity 1 mg
Datasheet Datasheet
Reactivity Mouse
Source Escherichia coli (E. coli)
Validations
Cat. No. ABIN7408927
Quantity 100 μg
Datasheet Datasheet

Synonyms and alternative names related to SGSH

N-sulfoglucosamine sulfohydrolase (SGSH), N-sulfoglucosamine sulfohydrolase (Sgsh), N-sulfoglucosamine sulfohydrolase (sulfamidase) (Sgsh), 4632406A19Rik, HSS, MPS3A, SFMD

Protein level used designations for SGSH

  • N-sulphoglucosamine sulphohydrolase
  • heparan sulfate sulfatase
  • mucopolysaccharidosis type IIIA
  • sulfoglucosamine sulfamidase
  • sulphamidase
  • N-sulfoglucosamine sulfohydrolase
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