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SGCG 抗体

(Sarcoglycan, gamma (35kDa Dystrophin-Associated Glycoprotein) (SGCG))
This gene encodes gamma-sarcoglycan, one of several sarcolemmal transmembrane glycoproteins that interact with dystrophin. The dystrophin-glycoprotein complex (DGC) spans the sarcolemma and is comprised of dystrophin, syntrophin, alpha- and beta-dystroglycans and sarcoglycans. The DGC provides a structural link between the subsarcolemmal cytoskeleton and the extracellular matrix of muscle cells. Defects in the encoded protein can lead to early onset autosomal recessive muscular dystrophy, in particular limb-girdle muscular dystrophy, type 2C (LGMD2C). [provided by RefSeq, Oct 2008].

35 results :

SGCG 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN520158
 
SGCG 适用: 人 WB, ELISA, IP 宿主: 小鼠 Monoclonal 3C5 unconjugated
产品编号 ABIN520160
 
SGCG 适用: 人, 小鼠, 大鼠 WB, IHC, IF, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6265040
 
SGCG 适用: 人 ELISA, IHC, IF 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7153555
 
SGCG 适用: 人 WB, IHC (p) 宿主: 兔 Polyclonal unconjugated
Pubmed 5 references
产品编号 ABIN1881799
 
SGCG 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN2565891
 
SGCG 适用: 人, 小鼠, 大鼠, 犬, Cow, 豚鼠, 马, 兔, 斑马鱼, Bat, 小鸡, 猴, Pig WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN320868
 
SGCG 适用: 人, 小鼠, 大鼠, 犬 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN630345
 
SGCG 适用: 人 宿主: 兔 Polyclonal FITC
产品编号 ABIN7153557
 
SGCG 适用: 人 ELISA 宿主: 兔 Polyclonal HRP
产品编号 ABIN7153558
 
SGCG 适用: 人 ELISA 宿主: 兔 Polyclonal Biotin
产品编号 ABIN7153556
 
SGCG 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7118790
 
SGCG 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7571253
 
Recent SGCG 适用: 人 ELISA 宿主: 山羊 Polyclonal unconjugated
产品编号 ABIN570751
 
SGCG 适用: 人 WB, IHC (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7464807
 
SGCG 适用: 人 WB, IHC, IP 宿主: 兔 Monoclonal R03-3G4R03-3G4 unconjugated Recombinant Antibody
产品编号 ABIN7542394
 
SGCG 适用: 人 IHC, IHC (fro) 宿主: 小鼠 Monoclonal 35DAG-21B5 unconjugated
产品编号 ABIN7538889
 
SGCG 适用: 人, 小鼠, 大鼠, 犬, Cow, 豚鼠, 马, 兔, 斑马鱼 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2781777
 
SGCG 适用: 人, 小鼠, 大鼠, 犬 WB, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2462796
 
SGCG 适用: 人 WB, IHC, IP 宿主: 兔 Monoclonal AbS34 unconjugated
产品编号 ABIN7604926
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • ELISA
    • Immunohistochemistry (IHC)
    • Immunoprecipitation (IP)
    • Immunofluorescence (IF)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunocytochemistry (ICC)
  • 适用
    • Human
    • Mouse
    • Rat
    • Dog
    • Cow
    • Guinea Pig
    • Horse
    • Rabbit
    • Zebrafish (Danio rerio)
    • Bat
    • Chicken
    • Monkey
    • Pig
  • 论文引用
  • 图像
  • Preservative free only
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
    • Goat
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 3C5
    • 35DAG-21B5
    • AbS34
    • R03-3G4R03-3G4
  • 抗原表位
    • AA 108-221
    • AA 1-291
    • AA 145-172
    • AA 151-200
    • AA 167-178
    • AA 191-290
    • AA 191-291
    • AA 68-291
    • C-Term
    • Internal Region
    • Middle Region
  • 标记
    • 非结合性
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • Biotin
    • FITC
    • HRP
  • 抗体亚型
    • IgG
    • Ig Fraction
    • IgG2a
    • IgG2a kappa
    • IgG2b
    • kappa
  • 蛋白类型
    • Recombinant Antibody
  • Format
    • Liquid
    • Lyophilized
  • Grade
    • Recent
  • Supplier
    • antibodies-online
    • Signalway
    • USBio
    • Abcepta
    • Aviva Systems Biology
    • Boster Bio
    • ProSci

Latest Publications for our SGCG 抗体

Chrzanowski, Vohra, Lee-McMullen, Batra, Spradlin, Morales, Forbes, Vandenborne, Barton, Walter: "Contrast-Enhanced Near-Infrared Optical Imaging Detects Exacerbation and Amelioration of Murine Muscular Dystrophy." in: Molecular imaging, Vol. 16, pp. 1536012117732439, (2018) (PubMed).

Rafii, Hagiwara, Mercado, Seo, Xu, Dugan, Owens, Hook, McQuillan, Young, Fallon: "Biglycan binds to alpha- and gamma-sarcoglycan and regulates their expression during development." in: Journal of cellular physiology, Vol. 209, Issue 2, pp. 439-47, (2006) (PubMed).

Dunham, Matthews, Burton, Ashurst, Howe, Ashcroft, Beare, Burford, Hunt, Griffiths-Jones, Jones, Keenan, Oliver, Scott, Ainscough, Almeida, Ambrose, Andrews, Ashwell, Babbage, Bagguley, Bailey et al.: "The DNA sequence and analysis of human chromosome 13. ..." in: Nature, Vol. 428, Issue 6982, pp. 522-8, (2004) (PubMed).

Thompson, Chan, Hack, Brosius, Rajala, Lidov, McNally, Watkins, Kunkel: "Filamin 2 (FLN2): A muscle-specific sarcoglycan interacting protein." in: The Journal of cell biology, Vol. 148, Issue 1, pp. 115-26, (2000) (PubMed).

Piccolo, Jeanpierre, Leturcq, Dodé, Azibi, Toutain, Merlini, Jarre, Navarro, Krishnamoorthy, Tomé, Urtizberea, Beckmann, Campbell, Kaplan: "A founder mutation in the gamma-sarcoglycan gene of gypsies possibly predating their migration out of India." in: Human molecular genetics, Vol. 5, Issue 12, pp. 2019-22, (1997) (PubMed).

McNally, Passos-Bueno, Bönnemann, Vainzof, de Sá Moreira, Lidov, Othmane, Denton, Vance, Zatz, Kunkel: "Mild and severe muscular dystrophy caused by a single gamma-sarcoglycan mutation." in: American journal of human genetics, Vol. 59, Issue 5, pp. 1040-7, (1996) (PubMed).

Noguchi, McNally, Ben Othmane, Hagiwara, Mizuno, Yoshida, Yamamoto, Bönnemann, Gussoni, Denton, Kyriakides, Middleton, Hentati, Ben Hamida, Nonaka, Vance, Kunkel, Ozawa: "Mutations in the dystrophin-associated protein gamma-sarcoglycan in chromosome 13 muscular dystrophy." in: Science (New York, N.Y.), Vol. 270, Issue 5237, pp. 819-22, (1995) (PubMed).

Aliases for SGCG 抗体

sarcoglycan, gamma (sgcg) 抗体
sarcoglycan gamma (SGCG) 抗体
sarcoglycan, gamma (35kDa dystrophin-associated glycoprotein) (SGCG) 抗体
sarcoglycan gamma (Sgcg) 抗体
sarcoglycan, gamma (dystrophin-associated glycoprotein) (Sgcg) 抗体
sarcoglycan, gamma (Sgcg) 抗体
35DAG 抗体
35kDa 抗体
5430420E18Rik 抗体
A4 抗体
AI642964 抗体
DAGA4 抗体
DMDA 抗体
DMDA1 抗体
Gamma-SG 抗体
gamma-SG 抗体
LGMD2C 抗体
MAM 抗体
SCARMD2 抗体
SCG3 抗体
TYPE 抗体
zgc:100924 抗体
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