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ISCU 抗体

(Iron-sulfur cluster assembly enzyme ISCU, mitochondrial (ISCU))
Iron-sulfur (Fe-S) clusters are necessary for several mitochondrial enzymes and other subcellular compartment proteins. They contain sulfur and iron, and are created via several steps that include cysteine desulfurases, iron donors, chaperones, and scaffold proteins. This gene encodes the two isomeric forms, ISCU1 and ISCU2, of the Fe-S cluster scaffold protein. Mutations in this gene have been found in patients with myopathy with severe exercise intolerance and myoglobinuria. [provided by RefSeq, Jul 2008].

28 results

ISCU 适用: 人 WB, ELISA, IF 宿主: 小鼠 Monoclonal 3B8-1C4 unconjugated
Pubmed 1 reference
产品编号 ABIN565100
 
ISCU 适用: 人, 小鼠, 大鼠 WB, IHC, IF, ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6262671
 
ISCU 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7157058
 
ISCU 适用: 人, 小鼠 WB 宿主: 兔 Polyclonal RB35591 unconjugated
Pubmed 5 references
产品编号 ABIN1881467
 
ISCU 适用: 人, 小鼠 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7261091
 
ISCU 适用: 人, 小鼠 WB, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7246487
 
ISCU 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN949116
 
ISCU 适用: 人, 小鼠, 大鼠, Cow, 犬, 豚鼠, 马, 兔, Bat, 小鸡, Hamster, 猴, 非洲爪蟾 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6746433
 
ISCU 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6142546
 
ISCU 适用: 人 宿主: 兔 Polyclonal FITC
产品编号 ABIN7157061
 
ISCU 适用: 人 ELISA 宿主: 兔 Polyclonal Biotin
产品编号 ABIN7157060
 
ISCU 适用: 人 ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7157059
 
ISCU 适用: 人 ELISA 宿主: 兔 Polyclonal HRP
产品编号 ABIN7157062
 
ISCU 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC, IF, IP 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7115516
 
ISCU 适用: 人, 小鼠 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1806975
 
ISCU 适用: 人 WB, IHC, IHC (p) 宿主: 小鼠 Monoclonal 4F5 unconjugated
产品编号 ABIN2610515
 
ISCU 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 3D12-1D10 unconjugated
产品编号 ABIN961458
 
ISCU 适用: 人 WB, IF, ICC, IHC (p) 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7468499
 
ISCU 适用: 人, 小鼠 WB, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2610513
 
ISCU 适用: 人, 小鼠 WB, ELISA 宿主: 兔 Polyclonal HRP
产品编号 ABIN1902599
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • ELISA
    • Immunohistochemistry (IHC)
    • Immunofluorescence (IF)
    • Immunocytochemistry (ICC)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunoprecipitation (IP)
  • 适用
    • Human
    • Mouse
    • Rat
    • Cow
    • Dog
    • Guinea Pig
    • Horse
    • Rabbit
    • Bat
    • Chicken
    • Goat
    • Hamster
    • Monkey
    • Xenopus laevis
    • Zebrafish (Danio rerio)
  • 论文引用
  • 图像
  • 仅无防腐剂
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • 3B8-1C4
    • 3D12-1D10
    • 4F5
    • RB35591
  • 抗原表位
    • AA 138-167
    • AA 35-167
    • AA 1-167
    • C-Term
    • N-Term
    • AA 1-142
    • AA 26-167
    • AA 26-168
    • Internal Region
  • 标记
    • 非结合性
    • FITC
    • Biotin
    • HRP
    • APC
    • PE
  • 抗体亚型
    • IgG
    • IgG1
    • Ig Fraction
    • IgG1 kappa
  • Format
    • Liquid
    • Lyophilized
  • Supplier
    • antibodies-online
    • Abbexa
    • Abcepta
    • Aviva Systems Biology
    • Enogene Biotech
    • USBio

Latest Publications for our ISCU 抗体

Heather, Cole, Tan, Ambrose, Pope, Abd-Jamil, Carter, Dodd, Yeoh, Schofield, Clarke: "Metabolic adaptation to chronic hypoxia in cardiac mitochondria." in: Basic research in cardiology, Vol. 107, Issue 3, pp. 268, (2012) (PubMed).

Okerlund, Kivimäe, Tong, Peng, Ullian, Cheyette: "Dact1 is a postsynaptic protein required for dendrite, spine, and excitatory synapse development in the mouse forebrain." in: The Journal of neuroscience : the official journal of the Society for Neuroscience, Vol. 30, Issue 12, pp. 4362-8, (2010) (PubMed).

Chan, Zhang, Hemann, Mahoney, Zweier, Loscalzo: "MicroRNA-210 controls mitochondrial metabolism during hypoxia by repressing the iron-sulfur cluster assembly proteins ISCU1/2." in: Cell metabolism, Vol. 10, Issue 4, pp. 273-84, (2009) (PubMed).

Kollberg, Tulinius, Melberg, Darin, Andersen, Holmgren, Oldfors, Holme: "Clinical manifestation and a new ISCU mutation in iron-sulphur cluster deficiency myopathy." in: Brain : a journal of neurology, Vol. 132, Issue Pt 8, pp. 2170-9, (2009) (PubMed).

Huang, Dizin, Cowan: "Mapping iron binding sites on human frataxin: implications for cluster assembly on the ISU Fe-S cluster scaffold protein." in: Journal of biological inorganic chemistry : JBIC : a publication of the Society of Biological Inorganic Chemistry, Vol. 13, Issue 5, pp. 825-36, (2008) (PubMed).

Mochel, Knight, Tong, Hernandez, Ayyad, Taivassalo, Andersen, Singleton, Rouault, Fischbeck, Haller: "Splice mutation in the iron-sulfur cluster scaffold protein ISCU causes myopathy with exercise intolerance." in: American journal of human genetics, Vol. 82, Issue 3, pp. 652-60, (2008) (PubMed).

Aliases for ISCU 抗体

iron-sulfur cluster assembly enzyme ISCU, mitochondrial (LOC409130) 抗体
iron-sulfur cluster assembly enzyme (ISCU) 抗体
iron-sulfur cluster assembly enzyme a (iscua) 抗体
iron-sulfur cluster assembly enzyme (Iscu) 抗体
2310020H20Rik 抗体
AA407971 抗体
HML 抗体
hnifU 抗体
ISU2 抗体
NIFU 抗体
Nifu 抗体
nifun 抗体
NIFUN 抗体
Nifun 抗体
RGD1309562 抗体
si:ch211-191d15.3 抗体
zC191D15.3 抗体
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