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GNS 抗体

(Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome. [provided by RefSeq, Jul 2008].

34 results :

GNS 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7160689
 
GNS 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN950002
 
GNS 适用: 人 IHC, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7160688
 
GNS 适用: 人 WB, IHC (p), FACS 宿主: 兔 Polyclonal RB19341 unconjugated
产品编号 ABIN390493
 
GNS 适用: 人, 小鼠, 大鼠, Cow, 山羊, 豚鼠, 马, 兔, 犬, 斑马鱼 WB, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN2782155
 
GNS 适用: 人 WB, IHC, FACS 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN3002692
 
GNS 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
产品编号 ABIN516125
 
GNS 适用: 人, 小鼠, 大鼠, Cow, 山羊, 豚鼠, 马, 兔, 犬, Bat, 猴 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6746256
 
GNS 适用: 人, 小鼠, 大鼠, Cow, 山羊, 豚鼠, 马, 兔, 斑马鱼, Bat, 猴 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN6738147
 
GNS 适用: 人, 小鼠, 大鼠 WB 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN635775
 
GNS 适用: 人, 小鼠, 大鼠 WB, ELISA 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN5693115
 
GNS 适用: 人 WB, IHC (p) 宿主: 兔 Polyclonal RB19340 unconjugated
产品编号 ABIN390494
 
GNS 适用: 人 ELISA, IF (cc), IF (p), IHC (p), IHC (fro), ICC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN1714381
 
GNS 适用: 人 ELISA, IHC (p), IHC (fro) 宿主: 兔 Polyclonal Biotin
产品编号 ABIN1700879
 
GNS 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 750
产品编号 ABIN5003752
 
GNS 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 680
产品编号 ABIN5003751
 
GNS 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 555
产品编号 ABIN1697255
 
GNS 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 488
产品编号 ABIN1695431
 
GNS 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 350
产品编号 ABIN1693612
 
GNS 适用: 人 IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 647
产品编号 ABIN1699066
 
  • 类型 Primary
    • Primary
  • 应用范围
    • Western Blotting (WB)
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • ELISA
    • Immunohistochemistry (IHC)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Flow Cytometry (FACS)
    • Immunocytochemistry (ICC)
    • Immunoprecipitation (IP)
    • Chemiluminescence Immunoassay (CLIA)
    • Enzyme Immunoassay (EIA)
  • 适用
    • Human
    • Mouse
    • Rat
    • Cow
    • Goat
    • Guinea Pig
    • Horse
    • Rabbit
    • Bat
    • Dog
    • Monkey
    • Zebrafish (Danio rerio)
    • Various Species
  • 图像
  • Carrier free only
  • 抗体来源
    • Rabbit
    • Mouse
    • Goat
  • 克隆形成能力
    • Polyclonal
    • Monoclonal
  • 克隆
    • C3
    • RB19340
    • RB19341
  • 抗原表位
    • AA 1-100
    • AA 1-552
    • AA 293-552
    • C-Term
    • AA 174-203
    • AA 190-270
    • AA 238-355
    • AA 283-313
    • AA 312-361
    • AA 37-552
    • AA 398-447
    • Middle Region
  • 标记
    • 非结合性
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Biotin
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
    • FITC
    • HRP
  • 抗体亚型
    • IgG
    • Ig Fraction
    • IgG1 kappa
  • Format
    • Liquid
    • Lyophilized
  • Supplier
    • antibodies-online
    • Abbexa
    • Abcepta
    • Acris
    • Aviva Systems Biology
    • Biomatik
    • Boster Bio

Aliases for GNS 抗体

glucosamine (N-acetyl)-6-sulfatase (GNS) 抗体
glucosamine (N-acetyl)-6-sulfatase (Gns) 抗体
glucosamine (N-acetyl)-6-sulfatase S homeolog (gns.S) 抗体
glucosamine (N-acetyl)-6-sulfatase (gns) 抗体
glucosamine (N-acetyl)-6-sulfatase a (gnsa) 抗体
N-acetylglucosamine-6-sulfatase (CpipJ_CPIJ000745) 抗体
N-acetylglucosamine-6-sulfatase (Sros_7372) 抗体
N-acetylglucosamine-6-sulfatase (VDBG_04409) 抗体
N-acetylglucosamine-6-sulfatase (Halhy_3165) 抗体
glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID), b (gnsb) 抗体
2610016K11Rik 抗体
AU042285 抗体
C87209 抗体
G6S 抗体
gns 抗体
N-acetylglucosamine-6-sulfatase 抗体
N28088 抗体
NV14559 抗体
wu:fi20h10 抗体
zgc:55370 抗体
zgc:114066 抗体
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