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GALNS 产品

(Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS))

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This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder. [provided by RefSeq, Jul 2008].

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Featured GALNS Categories

GALNS 抗体

High quality antibodies with extensive validation data.

GALNS ELISA试剂盒

Reliable ELISA kits for a wide range of species.

GALNS 蛋白

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended GALNS 抗体

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human, Mouse, Rat
Application WB, IF, IHC (p), ICC
Validations
  • (5)
Cat. No. ABIN2856743
Quantity 100 μL
Datasheet Datasheet
Reactivity Human, Mouse, Rat
Application WB, ELISA, IHC
Validations
  • (7)
Cat. No. ABIN5693230
Quantity 100 μg
Datasheet Datasheet
Reactivity Human
Application WB, IP
Validations
  • (3)
Cat. No. ABIN947896
Quantity 100 μL
Datasheet Datasheet

Recommended GALNS ELISA试剂盒

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
Cat. No. ABIN6966929
Quantity 96 tests
Datasheet Datasheet
Reactivity Mouse
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
Cat. No. ABIN1116112
Quantity 96 tests
Datasheet Datasheet
Reactivity Rat
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
Cat. No. ABIN1116114
Quantity 96 tests
Datasheet Datasheet

Recommended GALNS 蛋白

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1354724
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1354723
Quantity 25 μg
Datasheet Datasheet
Reactivity Human
Source Insect Cells
Validations
  • (1)
Cat. No. ABIN3080514
Quantity 1 mg
Datasheet Datasheet

Latest Publications for our GALNS Products

Bhattacharyya, Kotlo, Shukla, Danziger, Tobacman: "Distinct effects of N-acetylgalactosamine-4-sulfatase and galactose-6-sulfatase expression on chondroitin sulfates." in: The Journal of biological chemistry, Vol. 283, Issue 15, pp. 9523-30, (2008) (PubMed).

Chen, Kuo, Li, Bui, Peake, Sanders, Thibodeaux, Chu, Qian, Zhao, Bredt, Moller, Konrad, Beigneux, Young, Cao: "AGPAT6 is a novel microsomal glycerol-3-phosphate acyltransferase." in: The Journal of biological chemistry, Vol. 283, Issue 15, pp. 10048-57, (2008) (PubMed).

Houle, Tom, Mayes, Wagoner, Phillips, Silver: "Combining an autologous peripheral nervous system "bridge" and matrix modification by chondroitinase allows robust, functional regeneration beyond a hemisection lesion of the adult rat spinal cord." in: The Journal of neuroscience : the official journal of the Society for Neuroscience, Vol. 26, Issue 28, pp. 7405-15, (2006) (PubMed).

Synonyms and alternative names related to GALNS

galactosamine (N-acetyl)-6-sulfatase (GALNS), galactosamine (N-acetyl)-6-sulfate sulfatase (Galns), galactosamine (N-acetyl)-6-sulfatase (Galns), N-acetylgalactosamine-6-sulfatase (Celly_0425), galactosamine (N-acetyl)-6-sulfatase L homeolog (galns.L), galactosamine (N-acetyl)-6-sulfatase (galns), GalN6S, GALNAC6S, galns, GAS, mFLJ00319, MPS4A, zgc:158385

Protein level used designations for GALNS

  • N-acetylgalactosamine-6-sulfatase
  • N-acetylgalactosamine-6-sulfate sulfatase
  • chondroitinase
  • chondroitinsulfatase
  • galNAc6S sulfatase
  • galactose-6-sulfate sulfatase
  • GalNAc6S sulfatase
  • galactosamine (N-acetyl)-6-sulfate sulfatase (Morquio syndrome, mucopolysaccharidosis type IVA)
  • galactosamine (N-acetyl)-6-sulfatase L homeolog
  • galactosamine (N-acetyl)-6-sulfate sulfatase
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