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Dnah5 抗体

(Dynein, Axonemal, Heavy Chain 5 (Dnah5))
This gene encodes a dynein protein, which is part of a microtubule-associated motor protein complex consisting of heavy, light, and intermediate chains. This protein is an axonemal heavy chain dynein. It functions as a force-generating protein with ATPase activity, whereby the release of ADP is thought to produce the force-producing power stroke. Mutations in this gene cause primary ciliary dyskinesia type 3, as well as Kartagener syndrome, which are both diseases due to ciliary defects. [provided by RefSeq, Oct 2009].

Active filters:

  • 抗原: Dnah5
  • Primary
Catalog no. 产品 适用 宿主 / 克隆类型 应用 价格和交货时间
ABIN7150873
Dnah5 抗体 (AA 2364-2560) Dnah5 · Primary Antibody 人 兔 Polyclonal
  • IHC (Immunohistochemistry: 有验证图片)
  • IF (Immunofluorescence: 有验证图片)
  • ELISA (ELISA: 所列应用)
  • 100 μg
  • 50 μg
发货至: 中国
ABIN7094755
Dnah5 抗体 (Internal Region) Dnah5 · Primary Antibody 人, 小鼠, 大鼠 兔 Polyclonal
  • WB (Western Blotting: 所列应用)
  • 100 μL
  • 200 μL
发货至: 中国
ABIN7150876
Dnah5 抗体 (AA 2364-2560) (HRP) Dnah5 · Primary Antibody 人 兔 Polyclonal
  • ELISA (ELISA: 所列应用)
  • 100 μg
  • 50 μg
发货至: 中国
ABIN7150875
Dnah5 抗体 (AA 2364-2560) (FITC) Dnah5 · Primary Antibody 人 兔 Polyclonal
  • 100 μg
  • 50 μg
发货至: 中国
ABIN7150874
Dnah5 抗体 (AA 2364-2560) (Biotin) Dnah5 · Primary Antibody 人 兔 Polyclonal
  • ELISA (ELISA: 所列应用)
  • 100 μg
  • 50 μg
发货至: 中国
ABIN6086932
Dnah5 抗体 (AA 2364-2560) (FITC) Dnah5 · Primary Antibody 人 兔 Polyclonal
  • ELISA (ELISA: 所列应用)
  • 100 μL
  • 20 μL
  • 50 μL
发货至: 中国
Primary Antibody
  • IHC (Immunohistochemistry: 有验证图片)
  • IF (Immunofluorescence: 有验证图片)
  • ELISA (ELISA: 所列应用)
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
unconjugated
抗体亚型
IgG
抗原表位
AA 2364-2560
产品编号 ABIN7150873
100 μg (More quantities available)
发货至: 中国
获取报价
Primary Antibody
  • WB (Western Blotting: 所列应用)
适用
人, 小鼠, 大鼠
宿主
兔
克隆形成能力
Polyclonal
标记
unconjugated
抗体亚型
IgG
抗原表位
Internal Region
产品编号 ABIN7094755
100 μL (More quantities available)
发货至: 中国
获取报价
Primary Antibody
  • ELISA (ELISA: 所列应用)
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
HRP
抗体亚型
IgG
抗原表位
AA 2364-2560
产品编号 ABIN7150876
100 μg (More quantities available)
发货至: 中国
获取报价
Primary Antibody
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
FITC
抗体亚型
IgG
抗原表位
AA 2364-2560
产品编号 ABIN7150875
100 μg (More quantities available)
发货至: 中国
获取报价
Primary Antibody
  • ELISA (ELISA: 所列应用)
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
Biotin
抗体亚型
IgG
抗原表位
AA 2364-2560
产品编号 ABIN7150874
100 μg (More quantities available)
发货至: 中国
获取报价
Primary Antibody
  • ELISA (ELISA: 所列应用)
适用
人
宿主
兔
克隆形成能力
Polyclonal
标记
FITC
抗体亚型
IgG
抗原表位
AA 2364-2560
产品编号 ABIN6086932
100 μL (More quantities available)
发货至: 中国
获取报价

Latest Publications for our Dnah5 抗体

Onoufriadis, Shoemark, Schmidts, Patel, Jimenez, Liu, Thomas, Dixon, Hirst, Rutman, Burgoyne, Williams, Scully, Bolard, Lafitte, Beales, Hogg, Yang, Chung, Emes, OCallaghan, Bouvagnet, Mitchison: "Targeted NGS gene panel identifies mutations in RSPH1 causing primary ciliary dyskinesia and a common mechanism for ciliary central pair agenesis due to radial spoke defects." in: Human molecular genetics, Vol. 23, Issue 13, pp. 3362-74, (2014) (PubMed).

Diggle, Moore, Mali, zur Lage, Ait-Lounis, Schmidts, Shoemark, Garcia Munoz, Halachev, Gautier, Yeyati, Bonthron, Carr, Hayward, Markham, Hope, von Kriegsheim, Mitchison, Jackson, Durand, Reith et al.: "HEATR2 plays a conserved role in assembly of the ciliary motile apparatus. ..." in: PLoS genetics, Vol. 10, Issue 9, pp. e1004577, (2014) (PubMed).

Onoufriadis, Shoemark, Munye, James, Schmidts, Patel, Rosser, Bacchelli, Beales, Scambler, Hart, Danke-Roelse, Sloper, Hull, Hogg, Emes, Pals, Moore, Chung, Mitchison: "Combined exome and whole-genome sequencing identifies mutations in ARMC4 as a cause of primary ciliary dyskinesia with defects in the outer dynein arm." in: Journal of medical genetics, Vol. 51, Issue 1, pp. 61-7, (2013) (PubMed).

Aliases for Dnah5 抗体

dynein axonemal heavy chain 5 (DNAH5) 抗体
dynein, axonemal, heavy chain 5 (DNAH5) 抗体
dynein heavy chain 5, axonemal (LOC725479) 抗体
dynein heavy chain 8, axonemal (LOC100182341) 抗体
dynein heavy chain 5, axonemal (LOC100209217) 抗体
dynein heavy chain 5, axonemal (LOC100389549) 抗体
dynein axonemal heavy chain 5 S homeolog (dnah5.S) 抗体
dynein heavy chain 8, axonemal (LOC100638612) 抗体
dynein, axonemal, heavy chain 5 (Dnah5) 抗体
AU022615 抗体
b2b601Clo 抗体
b2b1134Clo 抗体
b2b1154Clo 抗体
b2b1537Clo 抗体
b2b1565Clo 抗体
CILD3 抗体
DLP5 抗体
DNAHC5 抗体
Dnahc5 抗体
Dnahc8 抗体
HL1 抗体
KTGNR 抗体
Mdnah5 抗体
mKIAA1603 抗体
PCD 抗体
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