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CPT2 产品

(Carnitine Palmitoyltransferase 2 (CPT2))

Categories

The protein encoded by this gene is a nuclear protein which is transported to the mitochondrial inner membrane. Together with carnitine palmitoyltransferase I, the encoded protein oxidizes long-chain fatty acids in the mitochondria. Defects in this gene are associated with mitochondrial long-chain fatty-acid (LCFA) oxidation disorders. [provided by RefSeq, Jul 2008].

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Featured CPT2 Categories

CPT2 抗体

High quality antibodies with extensive validation data.

CPT2 ELISA试剂盒

Reliable ELISA kits for a wide range of species.

CPT2 蛋白

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended CPT2 抗体

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human, Mouse, Rat
Application WB, ELISA, IHC, IF, ICC
Validations
  • (4)
Cat. No. ABIN6266193
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, IHC, IF
Validations
  • (4)
Cat. No. ABIN6138983
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB
Validations
  • (1)
  • (2)
Cat. No. ABIN947728
Quantity 50 μg
Datasheet Datasheet

Recommended CPT2 ELISA试剂盒

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
  • (1)
Cat. No. ABIN6954385
Quantity 96 tests
Datasheet Datasheet
Reactivity Rat
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
  • (1)
Cat. No. ABIN6954386
Quantity 96 tests
Datasheet Datasheet

Recommended CPT2 蛋白

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1350251
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1350253
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Escherichia coli (E. coli)
Validations
  • (1)
Cat. No. ABIN3078379
Quantity 1 mg
Datasheet Datasheet

Latest Publications for our CPT2 Products

Gu, Yao, Yang, Cai, Zheng, Wang, Yao, Yao: "Mitochondrial carnitine palmitoyl transferase-II inactivity aggravates lipid accumulation in rat hepatocarcinogenesis." in: World journal of gastroenterology, Vol. 23, Issue 2, pp. 256-264, (2017) (PubMed).

Lehmann, Zierz: "Normal protein content but abnormally inhibited enzyme activity in muscle carnitine palmitoyltransferase II deficiency." in: Journal of the neurological sciences, Vol. 339, Issue 1-2, pp. 183-8, (2014) (PubMed).

Console, Giangregorio, Indiveri, Tonazzi: "Carnitine/acylcarnitine translocase and carnitine palmitoyltransferase 2 form a complex in the inner mitochondrial membrane." in: Molecular and cellular biochemistry, Vol. 394, Issue 1-2, pp. 307-14, (2014) (PubMed).

Lan, Fu, Liu, Huang, Chang, Liu, Peng, Chen: "High frequency of ETFDH c.250G>A mutation in Taiwanese patients with late-onset lipid storage myopathy." in: Clinical genetics, Vol. 78, Issue 6, pp. 565-9, (2010) (PubMed).

Bailey, Xie, Do, Montpetit, Diaz, Mohan, Keavney, Yusuf, Gerstein, Engert, Anand: "Variation at the NFATC2 locus increases the risk of thiazolidinedione-induced edema in the Diabetes REduction Assessment with ramipril and rosiglitazone Medication (DREAM) study." in: Diabetes Care, Vol. 33, Issue 10, pp. 2250-3, (2010) (PubMed).

Ruaño, Thompson, Kane, Pullinger, Windemuth, Seip, Kocherla, Holford, Wu: "Physiogenomic analysis of statin-treated patients: domain-specific counter effects within the ACACB gene on low-density lipoprotein cholesterol?" in: Pharmacogenomics, Vol. 11, Issue 7, pp. 959-71, (2010) (PubMed).

Hogan, Vladutiu: "Malignant hyperthermia-like syndrome and carnitine palmitoyltransferase II deficiency with heterozygous R503C mutation." in: Anesthesia and analgesia, Vol. 109, Issue 4, pp. 1070-2, (2009) (PubMed).

Talmud, Drenos, Shah, Shah, Palmen, Verzilli, Gaunt, Pallas, Lovering, Li, Casas, Sofat, Kumari, Rodriguez, Johnson, Newhouse, Dominiczak, Samani, Caulfield, Sever, Stanton, Shields, Padmanabhan et al.: "Gene-centric association signals for lipids and apolipoproteins identified via the HumanCVD BeadChip. ..." in: American journal of human genetics, Vol. 85, Issue 5, pp. 628-42, (2009) (PubMed).

Isackson, Bennett, Lichter-Konecki, Willis, Nyhan, Sutton, Tein, Vladutiu: "CPT2 gene mutations resulting in lethal neonatal or severe infantile carnitine palmitoyltransferase II deficiency." in: Molecular genetics and metabolism, Vol. 94, Issue 4, pp. 422-7, (2008) (PubMed).

Deschauer, Wieser, Schröder, Zierz: "A novel nonsense mutation (515del4) in muscle carnitine palmitoyltransferase II deficiency." in: Molecular genetics and metabolism, Vol. 75, Issue 2, pp. 181-5, (2002) (PubMed).

Synonyms and alternative names related to CPT2

carnitine palmitoyltransferase 2 (CPT2), carnitine O-palmitoyltransferase 2, mitochondrial (LOC100214547), carnitine palmitoyltransferase 2 (Cpt2), carnitine palmitoyltransferase 2 S homeolog (cpt2.S), carnitine palmitoyltransferase 2 (cpt2), AI323697, cg2107, CPT1, CPTASE, CPTII, IIAE4, wu:fa03e08, wu:fb54a02, zgc:101627

Protein level used designations for CPT2

  • carnitine O-palmitoyltransferase 2, mitochondrial
  • carnitine palmitoyltransferase II
  • carnitine palmitoyltransferase 2
  • carnitine O-palmitoyltransferase
  • carnitine O-palmitoyltransferase 2, mitochondrial-like
  • CPT II
  • mitochondrial carnitine palmitoyltransferase II
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