DTNBP1 抗体 (N-Term)
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北京 101111
Quick Overview for DTNBP1 抗体 (N-Term) (ABIN966013)
抗原
See all DTNBP1 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- N-Term
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纯化方法
- Purified by antigen-specific affinity chromatography.
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免疫原
- Polyclonal antibody produced in rabbits immunizing with a synthetic peptide corresponding to N-terminal residues of human DTNBP1(Dystrobrevin binding protein 1)
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anti-Dystrobrevin Binding Protein 1 (DTNBP1) (AA 258-351) antibody
DTNBP1 适用: 人 IHC, ELISA, IF 宿主: 兔 Polyclonal unconjugated
anti-Dystrobrevin Binding Protein 1 (DTNBP1) (AA 179-319) antibodyDTNBP1 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Dystrobrevin Binding Protein 1 (DTNBP1) (C-Term) antibodyDTNBP1 适用: 人, 小鼠, 大鼠 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
anti-Dystrobrevin Binding Protein 1 (DTNBP1) (AA 1-100) antibodyDTNBP1 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 1B4 unconjugated
anti-Dystrobrevin Binding Protein 1 (DTNBP1) antibodyDTNBP1 适用: 人 WB, IHC (p), ICC, IF 宿主: 兔 Polyclonal unconjugated
anti-Dystrobrevin Binding Protein 1 (DTNBP1) (AA 110-305) antibodyDTNBP1 适用: 大鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Dystrobrevin Binding Protein 1 (DTNBP1) antibodyDTNBP1 适用: 人, 小鼠, 大鼠 WB, IHC, IF, IC 宿主: 兔 Polyclonal unconjugated
anti-Dystrobrevin Binding Protein 1 (DTNBP1) (AA 101-200) antibodyDTNBP1 适用: 大鼠 ELISA, IF (cc), IF (p), IHC (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
anti-Dystrobrevin Binding Protein 1 (DTNBP1) antibodyDTNBP1 适用: 人 WB 宿主: 小鼠 Monoclonal 25GB8285 unconjugated
anti-Dystrobrevin Binding Protein 1 (DTNBP1) (AA 8-38), (N-Term) antibodyDTNBP1 适用: 人, 小鼠 WB, IHC (p) 宿主: 兔 Polyclonal RB9243 unconjugated
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应用备注
- ELISA, Western blotting: 1µg/ml for 2hrs.
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- This antibody is stored in PBS, 50% glycerol
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储存液
- Sodium azide
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注意事项
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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- DTNBP1 (Dystrobrevin Binding Protein 1 (DTNBP1))
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别名
- DTNBP1(Dystrobrevin binding protein 1)
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背景
- DTNBP1(Dystrobrevin binding protein 1)plays a role in the biogenesis of lysosome-related organelles such as platelet dense granule and melanosomes. Dystrobrevin binding protein 1 binds to alpha and beta dystrobrevins that are components of the dystrophin-associated protein complex (DPC). It interacts with pallidin and MUTED. Dystrobrevin binding protein 1 is a part of the biogenesis of lysosome-related organelles complex 1 (BLOC-1). Defects in DTNBP1 are the cause of Hermansky-Pudlak syndrome 7 (HPS7). Hermansky-Pudlak syndrome (HPS) is a genetically heterogeneous, rare, autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS. Dystrobrevin binding protein 1 belongs to the dysbindin family.
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途径
- Synaptic Membrane, Regulation of G-Protein Coupled Receptor Protein Signaling
抗原
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