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HMGCL 抗体 (AA 41-140) (AbBy Fluor® 488)

This anti-HMGCL antibody is a 兔 多克隆 antibody detecting HMGCL in WB, IF (cc) 和 IF (p). Suitable for 小鼠.
产品编号 ABIN901010
发货至: 中国
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中国
北京 101111
No. 88 KeChuang 6th Street
Beijing Economic Technological Development Area
Room 801-803
4A Biotech Co.,Ltd.
Tel +86 (0512) 65829739 传真 +86 (010) 6788 5057

Quick Overview for HMGCL 抗体 (AA 41-140) (AbBy Fluor® 488) (ABIN901010)

抗原

See all HMGCL 抗体
HMGCL (3-Hydroxymethyl-3-Methylglutaryl-CoA Lyase (HMGCL))

适用

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小鼠

宿主

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克隆类型

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多克隆

标记

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This HMGCL antibody is conjugated to AbBy Fluor® 488

应用范围

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Western Blotting (WB), Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p))
  • 抗原表位

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    AA 41-140

    交叉反应

    小鼠

    预测反应

    Human,Rat,Dog,Horse,Chicken,Rabbit

    纯化方法

    Purified by Protein A.

    免疫原

    KLH conjugated synthetic peptide derived from human HMGCL

    亚型

    IgG
  • 应用备注

    IF(IHC-P) 1:50-200
    IF(IHC-F) 1:50-200
    IF(ICC) 1:50-200

    限制

    仅限研究用
  • 状态

    Liquid

    浓度

    1 μg/μL

    缓冲液

    Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.

    储存液

    ProClin

    注意事项

    This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.

    储存条件

    -20 °C

    储存方法

    Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.

    有效期

    12 months
  • 抗原

    HMGCL (3-Hydroxymethyl-3-Methylglutaryl-CoA Lyase (HMGCL))

    别名

    HMGCL

    背景

    Synonyms: 3 hydroxy 3 methylglutaryl CoA lyase, 3 hydroxy 3 methylglutaryl Coenzyme A lyase, 3 hydroxymethyl 3 methylglutaryl Coenzyme A lyase hydroxymethylglutaricaciduria, 3 hydroxymethyl 3 methylglutaryl Coenzyme A lyase, 3-hydroxy-3-methylglutarate-CoA lyase, HL, HMG CoA lyase, HMG CoA Lyase Deficiency, HMG-CoA lyase, HMGCL, HMGCL_HUMAN, Hydroxymethylglutaricaciduria, Hydroxymethylglutaryl CoA lyase, Hydroxymethylglutaryl CoA lyase mitochondrial, Hydroxymethylglutaryl-CoA lyase, mitochondrial, MS725, OTTHUMP00000044830.

    Background: Hydroxymethylglutaryl-CoA lyase (HMGCL) is found in fibroblasts, liver and lymphoblasts. It has a role in ketogenesis and leucine catabolism. Defects in HMGCL are the cause of 3-hydroxy-3-methylglutaryl-CoA lyase deficiency (hydroxymethylglutaricaciduria), an autosomal recessive disease which can lead to hypoglycemia and coma.

    基因ID

    2835
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