GAA 抗体 (N-Term)
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北京 101111
Quick Overview for GAA 抗体 (N-Term) (ABIN8101555)
抗原
See all GAA 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- N-Term
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原理
- GAA Antibody - N-terminal region
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序列
- RDLAPTPGAN LYGSHPFYLA LEDGGSAHGV FLLNSNAMDV VLQPSPALSW
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预测反应
- Dog: 86%, Guinea Pig: 100%, Horse: 86%, Human: 100%, Mouse: 100%, Rabbit: 100%, Rat: 100%
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纯化方法
- Affinity purified
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免疫原
- The immunogen is a synthetic peptide directed towards the N terminal region of human GAA
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anti-Glucosidase, Alpha, Acid (GAA) (AA 174-203), (N-Term) antibody
GAA 适用: 人 WB, IHC, IHC (p) 宿主: 兔 Polyclonal RB18979 unconjugated
anti-Glucosidase, Alpha, Acid (GAA) (AA 601-952) antibodyGAA 适用: 人 WB, IHC, ELISA, IF 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Alpha, Acid (GAA) (AA 595-770) antibodyGAA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Alpha, Acid (GAA) (AA 755-953) antibodyGAA 适用: 小鼠 IHC 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Alpha, Acid (GAA) (AA 851-952) antibodyGAA 适用: 人 ELISA 宿主: 小鼠 Monoclonal 3C6 unconjugated
anti-Glucosidase, Alpha, Acid (GAA) (Middle Region) antibodyGAA 适用: 人 WB, IHC 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Alpha, Acid (GAA) (AA 174-203) antibodyGAA 适用: 人 WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Alpha, Acid (GAA) (AA 1-952) antibodyGAA 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Alpha, Acid (GAA) (AA 541-640) antibodyGAA 适用: 人 WB, IF (cc), IF (p), IHC (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
anti-Glucosidase, Alpha, Acid (GAA) (AA 218-267) antibodyGAA 适用: 人, 小鼠, 大鼠, Cow, 犬, 豚鼠, 斑马鱼, Hamster, 猴, Pig WB 宿主: 兔 Polyclonal unconjugated
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应用备注
- Optimal working dilution should be determined by the investigator.
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说明
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We also sell a specific blocking peptide that can be used in combination with this antibody. You can find the blocking peptide under AAP44227-100UG
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 0.5 mg/mL
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缓冲液
- Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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注意事项
- prevent freeze-thaw cycles
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储存条件
- 4 °C,-20 °C
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储存方法
- For short term use, store at 2-8C up to 1 week. For long term storage, store at -20 °C in small aliquots to prevent freeze-thaw cycles.
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- GAA (Glucosidase, Alpha, Acid (GAA))
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别名
- GAA
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背景
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Background Information: This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants.
Gene Name: glucosidase, alpha, acid
Alternative Symbols: LYAG
Protein Name: lysosomal alpha-glucosidase
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分子量
- 104 kDa
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基因ID
- 2548
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NCBI登录号
- NP_000143
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UniProt
- P10253
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途径
- Cellular Glucan Metabolic Process
抗原
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