IDUA 抗体 (AA 1-87)
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北京 101111
Quick Overview for IDUA 抗体 (AA 1-87) (ABIN7999070)
抗原
See all IDUA 抗体适用
宿主
克隆类型
标记
应用范围
质量等级
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抗原表位
- AA 1-87
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原理
- Anti-IDUA Antibody
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交叉反应 (详细)
- No cross reactivity with other proteins.
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产品特性
- Anti-IDUA Antibody. Tested in ELISA, IF, IHC, WB, Flow Cytometry applications. This antibody reacts with Human, Mouse, Rat.
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纯化方法
- Immunogen affinity purified.
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免疫原
- E.coli-derived human INSIG1 recombinant protein (Position: M1-R87).
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亚型
- IgG
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应用备注
- Western blot, 0.25-0.5 μg/mL, Human, Mouse, Rat Immunohistochemistry (Paraffin-embedded Section), 2-5 μg/mL, Human, Mouse, Rat Immunofluorescence, 5 μg/mL, Human Flow Cytometry (Fixed), 1-3 μg/1x106 cells, Human ELISA, 0.1-0.5 μg/mL, -
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限制
- 仅限研究用
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状态
- Lyophilized
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溶解方式
- Adding 0.2 mL of distilled water will yield a concentration of 500 μg/mL.
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浓度
- 500 μg/mL
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缓冲液
- Each vial contains 4 mg Trehalose, 0.9 mg NaCl, 0.2 mg Na2HPO4.
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储存条件
- 4 °C,-20 °C
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储存方法
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At -20°C for one year from date of receipt. After reconstitution, at 4°C for one month.
It can also be aliquotted and stored frozen at -20°C for six months. Avoid repeated freezing and thawing. -
有效期
- 12 months
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- IDUA (Iduronidase, alpha-L- (IDUA))
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别名
- IDUA
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背景
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Background: This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I).
Gene Full Name: alpha-L-iduronidase
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分子量
- 73 kDa
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基因ID
- 3425
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UniProt
- P35475
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途径
- Glycosaminoglycan Metabolic Process
抗原
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