GNS 抗体 (AA 238-355) (Biotin)
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北京 101111
Quick Overview for GNS 抗体 (AA 238-355) (Biotin) (ABIN7993422)
抗原
See all GNS 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 238-355
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原理
- Anti-GNS Antibody Biotin Conjugated
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特异性
- No cross reactivity with other proteins.
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交叉反应 （详细）
- No cross-reactivity with other proteins.
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纯化方法
- Immunogen affinity purified.
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免疫原
- E. coli-derived human GNS recombinant protein (Position: W238-R355).
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亚型
- IgG
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anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 1-552) antibody
GNS 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 283-313) antibodyGNS 适用: 人 WB, FACS, IHC (p) 宿主: 兔 Polyclonal RB19341 unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 293-552) antibodyGNS 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 174-203) antibodyGNS 适用: 人 WB, IHC (p) 宿主: 兔 Polyclonal RB19340 unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 293-552) antibodyGNS 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 1-552) antibodyGNS 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 398-447) antibodyGNS 适用: 人, 小鼠, 大鼠, 斑马鱼, Cow, 山羊, 豚鼠, 马, 兔, Bat, 猴 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 312-361) antibodyGNS 适用: 人, 小鼠, 大鼠, Cow, 山羊, 豚鼠, 马, 兔, 犬, Bat, 猴 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (C-Term) antibodyGNS 适用: 人, 小鼠, 大鼠 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) antibodyGNS 适用: 人 WB, IHC, FACS 宿主: 兔 Polyclonal unconjugated
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应用备注
- Western blot, Optimal dilutions should be determined by end users. Immunohistochemistry (Paraffin-embedded Section), Optimal dilutions should be determined by end users. ELISA, Optimal dilutions should be determined by end users.
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限制
- 仅限研究用
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状态
- Liquid
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缓冲液
- Each vial contains 50 % glycerol, 0.9 % NaCl, 0.2 % Na2HPO4, 0.02 % Sodium azide.
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- At -20°C for one year from date of receipt. Avoid repeated freezing and thawing.
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有效期
- 12 months
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- GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
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别名
- GNS
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背景
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Background: N-acetylglucosamine-6-sulfatase, also known as glucosamine (N-acetyl)-6-sulfatase, is an enzyme that in humans is encoded by the GNS gene. The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
Gene Full Name: glucosamine (N-acetyl)-6-sulfatase
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基因ID
- 2799
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UniProt
- P15586
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途径
- Glycosaminoglycan Metabolic Process
抗原
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