IDUA 抗体 (AA 28-634)
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Quick Overview for IDUA 抗体 (AA 28-634) (ABIN7873280)
抗原
See all IDUA 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 28-634
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原理
- IDUA Antibody / Alpha-L-iduronidase
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纯化方法
- Antigen affinity purified
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免疫原
- An E.coli-derived human recombinant protein (amino acids A28-D634) was used as the immunogen for the IDUA antibody.
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亚型
- IgG
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应用备注
- Optimal dilution of the IDUA antibody should be determined by the researcher.
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限制
- 仅限研究用
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状态
- Lyophilized
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缓冲液
- 0.5 mg/mL if reconstituted with 0.2 mL sterile DI water
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储存条件
- 4 °C,-20 °C
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储存方法
- After reconstitution, the IDUA antibody can be stored for up to one month at 4oC. For long-term, aliquot and store at -20oC. Avoid repeated freezing and thawing.
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- IDUA (Iduronidase, alpha-L- (IDUA))
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别名
- IDUA
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背景
- This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I).
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UniProt
- P35475
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途径
- Glycosaminoglycan Metabolic Process
抗原
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