GNS 抗体 (AA 224-341)
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Quick Overview for GNS 抗体 (AA 224-341) (ABIN7872393)
抗原
See all GNS 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 224-341
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原理
- Zebrafish Gnsa Antibody / N-acetylglucosamine-6-sulfatase
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纯化方法
- Antigen affinity chromatography
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免疫原
- An E.coli-derived zebrafish Gnsa recombinant protein (amino acids W224-R341) was used as the immunogen for the Zebrafish Gnsa antibody.
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亚型
- Ig Fraction
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anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 1-552) antibody
GNS 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 293-552) antibodyGNS 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 283-313) antibodyGNS 适用: 人 WB, IHC (p), FACS 宿主: 兔 Polyclonal RB19341 unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 293-552) antibodyGNS 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 174-203) antibodyGNS 适用: 人 WB, IHC (p) 宿主: 兔 Polyclonal RB19340 unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (C-Term) antibodyGNS 适用: 人, 小鼠, 大鼠, 斑马鱼, Cow, 山羊, 豚鼠, 马, 兔, 犬 WB, IHC 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) antibodyGNS 适用: 人 WB, IHC, FACS 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 1-552) antibodyGNS 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 398-447) antibodyGNS 适用: 人, 小鼠, 大鼠, 斑马鱼, Cow, 山羊, 豚鼠, 马, 兔, Bat, 猴 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 312-361) antibodyGNS 适用: 人, 小鼠, 大鼠, Cow, 山羊, 豚鼠, 马, 兔, 犬, Bat, 猴 WB 宿主: 兔 Polyclonal unconjugated
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应用备注
- Optimal dilution of the Zebrafish Gnsa antibody should be determined by the researcher.
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限制
- 仅限研究用
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状态
- Lyophilized
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缓冲液
- 0.5 mg/mL if reconstituted with 0.2 mL sterile DI water
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储存条件
- 4 °C,-20 °C
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储存方法
- After reconstitution, the Zebrafish Gnsa antibody can be stored for up to one month at 4oC. For long-term, aliquot and store at -20oC. Avoid repeated freezing and thawing.
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- GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
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别名
- Gnsa
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背景
- N-acetylglucosamine-6-sulfatase, also known as glucosamine (N-acetyl)-6-sulfatase, is an enzyme that in humans is encoded by the GNS gene. The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
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UniProt
- Q4V902
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途径
- Glycosaminoglycan Metabolic Process
抗原
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