TIMM8A/DDP 抗体 (AA 1-50)
Quick Overview for TIMM8A/DDP 抗体 (AA 1-50) (ABIN7451527)
抗原
See all TIMM8A/DDP (TIMM8A) 抗体适用
宿主
克隆类型
标记
应用范围
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抗原表位
- AA 1-50
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原理
- Rabbit anti-TIMM8A Antibody, Affinity Purified
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纯化方法
- Affinity Purified
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免疫原
- Between AA 1 and 50
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亚型
- IgG
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应用备注
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IP: 2 - 10 μg/mg lysate
WB: Not recommended
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限制
- 仅限研究用
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浓度
- 1000 μg/mL
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缓冲液
- Tris-citrate/phosphate buffer, pH 7 to 8 containing 0.09 % Sodium Azide
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- 4 °C
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有效期
- 12 months
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- TIMM8A/DDP (TIMM8A) (Translocase of Inner Mitochondrial Membrane 8A (TIMM8A))
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别名
- TIMM8A
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背景
- Background: Translocase of inner mitochondrial membrane 8 homolog A (TIMM8A) is a translocase involved in the import and insertion of hydrophobic membrane proteins from the cytoplasm into the mitochondrial inner membrane. The TIMM8A gene is mutated in Mohr-Tranebjaerg syndrome/Deafness Dystonia Syndrome (MTS/DDS), and it is postulated that MTS/DDS is a mitochondrial disease caused by a defective mitochondrial protein import system. Defects in the TIMM8A gene also cause Jensen syndrome, an X-linked disease with opticoacoustic nerve atrophy and muscle weakness. Along with TIMM13, TIMM8A forms a 70 kDa heterohexamer [taken from NCBI Entrez Gene (Gene ID: 1678)].
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基因ID
- 1678
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NCBI登录号
- NP_004076
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UniProt
- O60220
抗原
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