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MCCC2 抗体 (AA 284-563)
This anti-MCCC2 antibody is a 兔 多克隆 antibody detecting MCCC2 in WB, IHC 和 IF. Suitable for 人.
Quick Overview for MCCC2 抗体 (AA 284-563) (ABIN7268494)
抗原
See all MCCC2 抗体
MCCC2
(Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
适用
All reactivities for MCCC2 抗体
人
宿主
All hosts for MCCC2 抗体
兔
克隆类型
All clonalities for MCCC2 抗体
多克隆
标记
All conjugates for MCCC2 抗体
This MCCC2 antibody is un-conjugated
应用范围
All applications for MCCC2 抗体
Western Blotting (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)
MCCC2抗体详情
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抗原表位
All epitopes for MCCC2 抗体
AA 284-563
原理
MCCC2 Rabbit pAb
序列
LHLTRKVVRN LNYQKKLDVT IEPSEEPLFP ADELYGIVGA NLKRSFDVRE VIARIVDGSR FTEFKAFYGD TLVTGFARIF GYPVGIVGNN GVLFSESAKK GTHFVQLCCQ RNIPLLFLQN ITGFMVGREY EAEGIAKDGA KMVAAVACAQ VPKITLIIGG SYGAGNYGMC GRAYSPRFLY IWPNARISVM GGEQAANVLA TITKDQRARE GKQFSSADEA ALKEPIIKKF EEEGNPYYSS ARVWDDGIID PADTRLVLGL SFSAALNAPI EKTDFGIFRM
交叉反应
人, 小鼠, 大鼠
产品特性
Polyclonal Antibodies
纯化方法
Affinity purification
免疫原
Recombinant fusion protein containing a sequence corresponding to amino acids 284-563 of human MCCC2 (NP_071415.1).
亚型
IgG
Alternatives
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使用细节
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应用备注
WB,1:500 - 1:2000,IHC,1:50 - 1:100,IF,1:50 - 1:100
限制
仅限研究用
贮存及处理
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状态
Liquid
缓冲液
PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
储存液
Sodium azide
注意事项
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
储存条件
-20 °C
储存方法
Store at -20°C. Avoid freeze / thaw cycles.
MCCC2目标详情
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抗原
MCCC2
(Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
别名
MCCC2
背景
This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.,MCCC2,MCCB,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,Amino acid metabolism,MCCC2
分子量
57kDa/61kDa
基因ID
64087
UniProt
Q9HCC0
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原发性抗体
anti-MCCC2 抗体 (AA 284-563) (ABIN7268494)
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